Quantitative isolation of α1AT mutant Z protein polymers from human and mouse livers and the effect of heat

Hepatology

Volumn 41, Issue 1, 2005, Pages 160-167

  An, Jae Koo ^a   Blomenkamp, Keith ^a   Lindblad, Douglas ^a   Teckman, Jeffrey H ^a,b  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA 1 ANTITRYPSIN; ALPHA 1 ANTITRYPSIN Z PROTEIN; MUTANT PROTEIN; POLYMER; SECRETORY PROTEIN; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; CELL INCLUSION; FEVER; GENE; HEAT; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; LIVER INJURY; NONHUMAN; PERIODIC ACID SCHIFF STAIN; POLYMERIZATION; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN CONFORMATION; PROTEIN ISOLATION; PROTEIN SYNTHESIS; QUANTITATIVE ANALYSIS; STEADY STATE; Z GENE; ANIMAL; CHEMISTRY; GENETICS; ISOLATION AND PURIFICATION; LIVER; LIVER DISEASE; METABOLISM; MOUSE; MUTATION; PATHOLOGY;

ALPHA 1-ANTITRYPSIN; ANIMALS; HEAT; HUMANS; LIVER; LIVER DISEASES; MICE; MUTATION; PERIODIC ACID-SCHIFF REACTION; POLYMERS;

EID: 11244346111     PISSN: 02709139     EISSN: None     Source Type: Journal    
DOI: 10.1002/hep.20508     Document Type: Article

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