Retention of mutant α1-antitrypsin Z in endoplasmic reticulum is associated with an autophagic response

American Journal of Physiology - Gastrointestinal and Liver Physiology

Volumn 279, Issue 5 42-5, 2000, Pages

  Teckman, Jeffrey H ^a   Perlmutter, David H ^a  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

Author keywords

Autophagy; Liver disease; Quality control

Indexed keywords

ALPHA 1 ANTITRYPSIN; ALPHA 1 ANTITRYPSIN Z; MUTANT PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; AUTOPHAGY; CARCINOGENESIS; CELL PROTECTION; CHRONIC HEPATITIS; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; FIBROBLAST; HUMAN; HUMAN CELL; IMMUNOELECTRON MICROSCOPY; LIVER CELL CARCINOMA; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION;

EID: 0033671965     PISSN: 01931857     EISSN: None     Source Type: Journal    
DOI: 10.1152/ajpgi.2000.279.5.g961     Document Type: Article

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