α1-antitrypsin polymerization and the serpinopathies: Pathobiology and prospects for therapy

Journal of Clinical Investigation

Volumn 110, Issue 11, 2002, Pages 1585-1590

  Lomas, David A ^a,b   Mahadeva, Ravi ^a  

^a UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^b WELLCOME TRUST SANGER INSTITUTE   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA 1 ANTITRYPSIN; SERINE PROTEINASE INHIBITOR;

ALPHA 1 ANTITRYPSIN DEFICIENCY; EMPHYSEMA; IN VIVO STUDY; MOLECULAR BIOLOGY; PATHOLOGY; POLYMERIZATION; PRIORITY JOURNAL; REVIEW; CHEMICAL STRUCTURE; CHEMISTRY; HUMAN; LIVER; MACROMOLECULE; METABOLISM; PROTEIN SECONDARY STRUCTURE;

ALPHA 1-ANTITRYPSIN; ALPHA 1-ANTITRYPSIN DEFICIENCY; HUMANS; LIVER; MACROMOLECULAR SUBSTANCES; MODELS, MOLECULAR; PROTEIN STRUCTURE, SECONDARY; SERINE PROTEINASE INHIBITORS; SERPINS;

EID: 85047684827     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI0216782     Document Type: Review

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