Mitochondrial iron trafficking and the integration of iron metabolism between the mitochondrion and cytosol

Proceedings of the National Academy of Sciences of the United States of America

Volumn 107, Issue 24, 2010, Pages 10775-10782

  Richardson, Des R ^a   Lane, Darius J R ^a   Becker, Erika M ^a   Huang, Michael L H ^a   Whitnall, Megan ^a   Rahmanto, Yohan Suryo ^a   Sheftel, Alex D ^b   Ponka, Prem ^c,d  

^a UNIVERSITY OF SYDNEY   (Australia)

^b PHILIPPS UNIVERSITY MARBURG   (Germany)

^c MCGILL UNIVERSITY   (Canada)

^d MCGILL UNIVERSITY   (Canada)

Author keywords

Frataxin; Friedreich's ataxia; Heme; Iron sulfur cluster; Sideroblastic anemia

Indexed keywords

ALAS PROTEIN; FERRITIN; FRATAXIN; HEME; IRON BINDING PROTEIN; IRON REGULATORY FACTOR; IRON SULFUR CLUSTER; MITOFERRIN 1; MITOFERRIN 2; MULTIENZYME COMPLEX; MYOTONIC DYSTROPHY KINASE RELATED CDC42 BINDING KINASE ALPHA; PROTEIN; PROTEIN KINASE; PROTOPORPHYRIN; SLC22A4 PROTEIN; SLC25A39 PROTEIN; SULFUR DERIVATIVE; TMEM14C PROTEIN; TRANSFER RNA; TRANSFERRIN RECEPTOR; UNCLASSIFIED DRUG;

CELL COMMUNICATION; CELL DIFFERENTIATION; CELL ORGANELLE; CYTOSOL; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ERYTHROID CELL; FRIEDREICH ATAXIA; HOMEOSTASIS; HUMAN; HYDROLYSIS; IRON METABOLISM; IRON RESPONSIVE ELEMENT; IRON STORAGE; IRON TRANSPORT; MITOCHONDRION; OXIDATION REDUCTION REACTION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SYNTHESIS; REFRACTORY ANEMIA WITH RINGED SIDEROBLASTS; RETICULOCYTE; REVIEW; SIDEROBLASTIC ANEMIA; SIGNAL TRANSDUCTION; WHOLE CELL; X LINKED SIDEROBLASTIC ANEMIA;

ANEMIA, SIDEROBLASTIC; ANIMALS; BIOLOGICAL TRANSPORT, ACTIVE; CYTOSOL; FRIEDREICH ATAXIA; HEME; HOMEOSTASIS; HUMANS; IRON; IRON-BINDING PROTEINS; IRON-SULFUR PROTEINS; MITOCHONDRIA; MODELS, BIOLOGICAL; RECEPTORS, TRANSFERRIN; TRANSFERRIN;

EID: 77954627973     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.0912925107     Document Type: Review

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