Iron-dependent regulation of frataxin expression: Implications for treatment of Friedreich ataxia

Human Molecular Genetics

Volumn 17, Issue 15, 2008, Pages 2265-2273

  Li, Kuanyu ^a   Besse, Edward K ^a   Ha, Dung ^a   Kovtunovych, Gennadiy ^a   Rouault, Tracey A ^a  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DEFEROXAMINE MESYLATE; FERRIC AMMONIUM CITRATE; FRATAXIN; IRON; IRON CHELATING AGENT; IRON REGULATORY PROTEIN 1; IRON REGULATORY PROTEIN 2; MESSENGER RNA; SULFUR;

ARTICLE; CELL STRAIN HEK293; CONTROLLED STUDY; CYTOSOL; DEGENERATIVE DISEASE; FIBROBLAST; FRIEDREICH ATAXIA; GENE EXPRESSION REGULATION; HUMAN; HUMAN CELL; INTRON; IRON DEPLETION; IRON OVERLOAD; LYMPHOBLAST; MITOCHONDRION; NORTHERN BLOTTING; PATHOGENESIS; PRIORITY JOURNAL; RECEPTOR BINDING; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; TRINUCLEOTIDE REPEAT; WESTERN BLOTTING;

CELL LINE; CYTOSOL; DEFEROXAMINE; FIBROBLASTS; FRIEDREICH ATAXIA; GENE EXPRESSION REGULATION; HUMANS; IRON; IRON CHELATING AGENTS; IRON OVERLOAD; IRON REGULATORY PROTEIN 2; IRON-BINDING PROTEINS; LYMPHOCYTES; MITOCHONDRIA; RNA, MESSENGER;

EID: 47249127786     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddn127     Document Type: Article

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