The ins and outs of mitochondrial iron-loading: The metabolic defect in Friedreich's ataxia

Journal of Molecular Medicine

Volumn 88, Issue 4, 2010, Pages 323-329

  Richardson, Des R ^a   Huang, Michael L H ^a   Whitnall, Megan ^a   Becker, Erika M ^a   Ponka, Prem ^b   Suryo Rahmanto, Yohan ^a  

^a UNIVERSITY OF SYDNEY   (Australia)

^b MCGILL UNIVERSITY   (Canada)

Author keywords

Heme; Iron; Iron metabolism; Iron sulfur cluster; Transferrin receptor 1

Indexed keywords

CD71 ANTIGEN; FERROPORTIN; FRATAXIN; INCRETIN; IRON; SULFUR; TRANSFERRIN;

CARDIOVASCULAR DISEASE; DEGENERATIVE DISEASE; DOWN REGULATION; FRIEDREICH ATAXIA; GENE DELETION; HEME SYNTHESIS; IRON METABOLISM; IRON OVERLOAD; IRON STORAGE; IRON TRANSPORT; KNOCKOUT MOUSE; METABOLIC DISORDER; MITOCHONDRION; NONHUMAN; PROTEIN EXPRESSION; REVIEW; UPREGULATION;

ANIMALS; CATION TRANSPORT PROTEINS; CYTOSOL; FRIEDREICH ATAXIA; HEME; HUMANS; IRON; IRON OVERLOAD; IRON-BINDING PROTEINS; IRON-SULFUR PROTEINS; MICE; MITOCHONDRIA; MODELS, BIOLOGICAL; MUTATION; RECEPTORS, TRANSFERRIN;

EID: 77951253200     PISSN: 09462716     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00109-009-0565-x     Document Type: Review

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