Mitochondrial functional alterations in relation to pathophysiology of Huntington's disease

Journal of Bioenergetics and Biomembranes

Volumn 42, Issue 3, 2010, Pages 217-226

  Pandey, Mritunjay ^a,b   Mohanakumar, Kochupurackal P ^a   Usha, Rajamma ^b  

^a INDIAN INSTITUTE OF CHEMICAL BIOLOGY   (India)

^b Manovikas Kendra Rehabilitation and Research Institute for the Handicapped   (India)

Author keywords

Calcium imbalance; Contribution of dopamine; Electron transport chain; Mitochondrial membrane potential; Mitochondrial trafficking; Mutant Huntington; Oxidative stress

Indexed keywords

DOPAMINE; MULTIENZYME COMPLEX;

APOPTOSIS; AUTOPSY; BRAIN MITOCHONDRION; CALCIUM BALANCE; ENZYME ACTIVITY; HUMAN; HUNTINGTON CHOREA; NERVE DEGENERATION; NERVE FIBER; NONHUMAN; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PHENOTYPE; RESPIRATORY CHAIN; REVIEW; ANIMAL; BRAIN; HUNTINGTON DISEASE; MITOCHONDRION; PATHOLOGY; PHYSIOLOGY;

ANIMALS; BRAIN; ELECTRON TRANSPORT CHAIN COMPLEX PROTEINS; HUMANS; HUNTINGTON DISEASE; MITOCHONDRIA; NERVE DEGENERATION;

ANIMALIA; INVERTEBRATA; VERTEBRATA;

EID: 77954425719     PISSN: 0145479X     EISSN: 15736881     Source Type: Journal    
DOI: 10.1007/s10863-010-9288-5     Document Type: Review

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