-
1
-
-
0027976996
-
Increased body temperature accelerates aggregation of the Leu-68-->Gln mutant cystatin C, the amyloid-forming protein in hereditary cystatin C amyloid angiopathy
-
Abrahamson M., and Grubb A. Increased body temperature accelerates aggregation of the Leu-68-->Gln mutant cystatin C, the amyloid-forming protein in hereditary cystatin C amyloid angiopathy. Proc. Natl. Acad. Sci. U.S.A. 91 (1994) 1416-1420
-
(1994)
Proc. Natl. Acad. Sci. U.S.A.
, vol.91
, pp. 1416-1420
-
-
Abrahamson, M.1
Grubb, A.2
-
2
-
-
0345760069
-
Characterization of β-amyloid assemblies in druzen: the deposits associated with aging and aged-related macular degeneration
-
Anderson D.H., Talaga K.C., Rivest A.J., Barron E., Hageman G.S., and Johnson L.V. Characterization of β-amyloid assemblies in druzen: the deposits associated with aging and aged-related macular degeneration. Exp. Eye Res. 78 (2004) 243-256
-
(2004)
Exp. Eye Res.
, vol.78
, pp. 243-256
-
-
Anderson, D.H.1
Talaga, K.C.2
Rivest, A.J.3
Barron, E.4
Hageman, G.S.5
Johnson, L.V.6
-
3
-
-
0015361994
-
The formation and stabilization of protein structure. The sixth jubilee lecture
-
Anfinsen C.B. The formation and stabilization of protein structure. The sixth jubilee lecture. Biochem. J. 128 (1972) 737-749
-
(1972)
Biochem. J.
, vol.128
, pp. 737-749
-
-
Anfinsen, C.B.1
-
4
-
-
0015859467
-
Principles that govern the folding of protein chains
-
Anfinsen C.B. Principles that govern the folding of protein chains. Science 181 (1973) 223-230
-
(1973)
Science
, vol.181
, pp. 223-230
-
-
Anfinsen, C.B.1
-
5
-
-
20344373420
-
Lactoferrin Glu561Asp facilitates secondary amyloidosis in the cornea
-
Araki-Sasaki K., Ando Y., Nakamura M., Kitagawa K., Ikemizu S., Kawaji T., Yamashita T., Ueda M., Hirano K., Yamada M., Matsumoto K., Kinoshita S., and Tanihara H. Lactoferrin Glu561Asp facilitates secondary amyloidosis in the cornea. Br. J. Ophthalmol. 89 (2005) 684-688
-
(2005)
Br. J. Ophthalmol.
, vol.89
, pp. 684-688
-
-
Araki-Sasaki, K.1
Ando, Y.2
Nakamura, M.3
Kitagawa, K.4
Ikemizu, S.5
Kawaji, T.6
Yamashita, T.7
Ueda, M.8
Hirano, K.9
Yamada, M.10
Matsumoto, K.11
Kinoshita, S.12
Tanihara, H.13
-
7
-
-
1042288284
-
Tau paired helical filaments from Alzheimer's disease brain and assembled in vitro are based on beta-structure in the core domain
-
Barghorn S., Davies P., and Mandelkow E. Tau paired helical filaments from Alzheimer's disease brain and assembled in vitro are based on beta-structure in the core domain. Biochemistry 43 (2004) 1694-1703
-
(2004)
Biochemistry
, vol.43
, pp. 1694-1703
-
-
Barghorn, S.1
Davies, P.2
Mandelkow, E.3
-
8
-
-
0346093906
-
Isolated vitreoretinal amyloidosis in the absence of transthyretin mutations
-
Barouch F.C., Benson M.D., and Mukai S. Isolated vitreoretinal amyloidosis in the absence of transthyretin mutations. Arch. Ophthalmol. 122 (2004) 123-125
-
(2004)
Arch. Ophthalmol.
, vol.122
, pp. 123-125
-
-
Barouch, F.C.1
Benson, M.D.2
Mukai, S.3
-
9
-
-
33644968545
-
Glutamic acid-rich proteins of rod photoreceptors are natively unfolded
-
Batra-Safferling R., Abarca-Heidemann K., Körschen H.G., Tziatzios C., Stoldt M., Budyak I., Willbold D., Schwalbe H., Klein-Seetharaman J., and Kaupp U.B. Glutamic acid-rich proteins of rod photoreceptors are natively unfolded. J. Biol. Chem. 281 (2006) 1449-1460
-
(2006)
J. Biol. Chem.
, vol.281
, pp. 1449-1460
-
-
Batra-Safferling, R.1
Abarca-Heidemann, K.2
Körschen, H.G.3
Tziatzios, C.4
Stoldt, M.5
Budyak, I.6
Willbold, D.7
Schwalbe, H.8
Klein-Seetharaman, J.9
Kaupp, U.B.10
-
10
-
-
0348240034
-
Vitreous amyloidosis
-
Albert D.M., and Jakobiec F.A. (Eds), WB Saunders, Philadelphia, PA
-
Bhisitkul R.B., and Mukai S. Vitreous amyloidosis. In: Albert D.M., and Jakobiec F.A. (Eds). Principles and Practice of Ophthalmology. 2nd ed. (2000), WB Saunders, Philadelphia, PA 2530-2539
-
(2000)
Principles and Practice of Ophthalmology. 2nd ed.
, pp. 2530-2539
-
-
Bhisitkul, R.B.1
Mukai, S.2
-
11
-
-
0031056829
-
Instability, unfolding and aggregation of human lysozyme variants underlying amyloid fibrillogenesis
-
Booth D.R., Sunde Belotti M.V., Robinson C.V., Hutchinson W.L., Fraser P.E., Hawkins P.N., Dobson C.M., Radford S.E., Blake C.C., and Pepys M.B. Instability, unfolding and aggregation of human lysozyme variants underlying amyloid fibrillogenesis. Nature 385 (1997) 787-793
-
(1997)
Nature
, vol.385
, pp. 787-793
-
-
Booth, D.R.1
Sunde Belotti, M.V.2
Robinson, C.V.3
Hutchinson, W.L.4
Fraser, P.E.5
Hawkins, P.N.6
Dobson, C.M.7
Radford, S.E.8
Blake, C.C.9
Pepys, M.B.10
-
12
-
-
59549086901
-
A dominant vimentin mutant upregulates Hsp70 and the activity of the ubiquitin-proteasome system, and causes posterior cataracts in transgenic mice
-
Bornheim R., Müller M., Reuter U., Herrmann H., Büssow H., and Magin T.M. A dominant vimentin mutant upregulates Hsp70 and the activity of the ubiquitin-proteasome system, and causes posterior cataracts in transgenic mice. J. Cell Sci. 121 (2008) 3737-3746
-
(2008)
J. Cell Sci.
, vol.121
, pp. 3737-3746
-
-
Bornheim, R.1
Müller, M.2
Reuter, U.3
Herrmann, H.4
Büssow, H.5
Magin, T.M.6
-
13
-
-
33646127577
-
Molecular chaperones and protein quality control
-
Bukau B., Weissman J., and Horwich A. Molecular chaperones and protein quality control. Cell 125 (2006) 443-451
-
(2006)
Cell
, vol.125
, pp. 443-451
-
-
Bukau, B.1
Weissman, J.2
Horwich, A.3
-
14
-
-
0030841343
-
Conformational disease
-
Carrell R.W., and Lomas D.A. Conformational disease. Lancet 350 (1997) 134-138
-
(1997)
Lancet
, vol.350
, pp. 134-138
-
-
Carrell, R.W.1
Lomas, D.A.2
-
15
-
-
0038819926
-
The chaperone environment at the cytoplasmic face of the endoplasmic reticulum can modulate rhodopsin processing and inclusion formation
-
Chapple J.P., and Cheetham M.E. The chaperone environment at the cytoplasmic face of the endoplasmic reticulum can modulate rhodopsin processing and inclusion formation. J. Biol. Chem. 278 (2003) 19087-19094
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 19087-19094
-
-
Chapple, J.P.1
Cheetham, M.E.2
-
16
-
-
0034853668
-
Unfolding retinal dystrophies: a role for molecular chaperones?
-
Chapple J.P., Grayson C., Hardcastle A.J., Saliba R.S., vanderSpuy J., and Cheesam M.E. Unfolding retinal dystrophies: a role for molecular chaperones?. Trends Mol. Med. 7 (2001) 414-421
-
(2001)
Trends Mol. Med.
, vol.7
, pp. 414-421
-
-
Chapple, J.P.1
Grayson, C.2
Hardcastle, A.J.3
Saliba, R.S.4
vanderSpuy, J.5
Cheesam, M.E.6
-
18
-
-
0031464278
-
Molecular evidence for the involvement of alpha crystallin in the coloration/crosslinking of crystallins in age related nuclear cataract
-
Chen Y.C., Reid G.E., Simpson R.J., and Truscott R.J. Molecular evidence for the involvement of alpha crystallin in the coloration/crosslinking of crystallins in age related nuclear cataract. Exp. Eye Res. 65 (1997) 835-840
-
(1997)
Exp. Eye Res.
, vol.65
, pp. 835-840
-
-
Chen, Y.C.1
Reid, G.E.2
Simpson, R.J.3
Truscott, R.J.4
-
19
-
-
30344461634
-
Scrapie pathogenesis in brain and retina: effects of prion protein expression in neurons and astrocytes
-
Chesebro B., Race R., and Kercher L. Scrapie pathogenesis in brain and retina: effects of prion protein expression in neurons and astrocytes. J. Neurovirol. 11 (2005) 476-480
-
(2005)
J. Neurovirol.
, vol.11
, pp. 476-480
-
-
Chesebro, B.1
Race, R.2
Kercher, L.3
-
20
-
-
33746377894
-
Protein misfolding, functional amyloid, and human disease
-
Chiti F., and Dobson C.M. Protein misfolding, functional amyloid, and human disease. Ann. Rev. Biochem. 75 (2006) 333-366
-
(2006)
Ann. Rev. Biochem.
, vol.75
, pp. 333-366
-
-
Chiti, F.1
Dobson, C.M.2
-
21
-
-
0346670134
-
A model of FAS1 domain 4 of the corneal protein βig-h3 gives a clearer view on corneal dystrophies
-
Clout N.J., and Hohenester E. A model of FAS1 domain 4 of the corneal protein βig-h3 gives a clearer view on corneal dystrophies. Mol. Vis. 9 (2003) 440-448
-
(2003)
Mol. Vis.
, vol.9
, pp. 440-448
-
-
Clout, N.J.1
Hohenester, E.2
-
22
-
-
33947517558
-
AGGRESCAN: a server for the prediction and evaluation of "hot spots" of aggregation in polypeptides
-
Conchillo-Solé O., de Groot N.S., Avilés F.X., Vendrell J., Daura X., and Ventura S. AGGRESCAN: a server for the prediction and evaluation of "hot spots" of aggregation in polypeptides. BMC Bioinformatics 8 (2007) 65-81
-
(2007)
BMC Bioinformatics
, vol.8
, pp. 65-81
-
-
Conchillo-Solé, O.1
de Groot, N.S.2
Avilés, F.X.3
Vendrell, J.4
Daura, X.5
Ventura, S.6
-
23
-
-
0032540327
-
Stabilization of α-synuclein secondary structure upon binding to synthetic membranes
-
Davidson W.S., Jonas A., Clayton D.F., and George J.M. Stabilization of α-synuclein secondary structure upon binding to synthetic membranes. J. Biol. Chem. 273 (1998) 9443-9449
-
(1998)
J. Biol. Chem.
, vol.273
, pp. 9443-9449
-
-
Davidson, W.S.1
Jonas, A.2
Clayton, D.F.3
George, J.M.4
-
24
-
-
1842482905
-
Pharmaceutical strategies against amyloidosis: old and new drugs in targeting a protein misfolding disease
-
DeLorenzi E., Giorgetti S., Grossi S., Merlini G., Caccialanza G., and Belotti V. Pharmaceutical strategies against amyloidosis: old and new drugs in targeting a protein misfolding disease. Curr. Med. Chem. 204 (2004) 1065-1084
-
(2004)
Curr. Med. Chem.
, vol.204
, pp. 1065-1084
-
-
DeLorenzi, E.1
Giorgetti, S.2
Grossi, S.3
Merlini, G.4
Caccialanza, G.5
Belotti, V.6
-
25
-
-
0037096983
-
Effects of modifications of α-crystallin on its chaperone and other properties
-
Derham B.K., and Harding J.J. Effects of modifications of α-crystallin on its chaperone and other properties. Biochem. J. 364 (2002) 711-717
-
(2002)
Biochem. J.
, vol.364
, pp. 711-717
-
-
Derham, B.K.1
Harding, J.J.2
-
26
-
-
1842298212
-
From Levinthal to pathways to funnels
-
Dill K.A., and Chan H.S. From Levinthal to pathways to funnels. Nat. Struct. Biol. 4 (1997) 10-19
-
(1997)
Nat. Struct. Biol.
, vol.4
, pp. 10-19
-
-
Dill, K.A.1
Chan, H.S.2
-
27
-
-
38749112528
-
Targeting age-related macular degeneration with AD based immunotherapies: anti-amyloid-β antibody attenuates pathologies in an age-related macular degeneration mouse model
-
Ding J., Lin J., Mace B.E., Herrmann R., Sullivan P., and Rickman C.B. Targeting age-related macular degeneration with AD based immunotherapies: anti-amyloid-β antibody attenuates pathologies in an age-related macular degeneration mouse model. Vision Res. 48 (2008) 339-345
-
(2008)
Vision Res.
, vol.48
, pp. 339-345
-
-
Ding, J.1
Lin, J.2
Mace, B.E.3
Herrmann, R.4
Sullivan, P.5
Rickman, C.B.6
-
28
-
-
0033200063
-
Protein misfolding, evolution and disease
-
Dobson C.M. Protein misfolding, evolution and disease. TIBS 24 (1999) 329-332
-
(1999)
TIBS
, vol.24
, pp. 329-332
-
-
Dobson, C.M.1
-
29
-
-
0035961329
-
The structural basis of protein folding and its links with human disease
-
Dobson C.M. The structural basis of protein folding and its links with human disease. Philos. Trans. R. Soc. Lond. B: Biol. Sci. 356 (2001) 133-145
-
(2001)
Philos. Trans. R. Soc. Lond. B: Biol. Sci.
, vol.356
, pp. 133-145
-
-
Dobson, C.M.1
-
30
-
-
0037102362
-
Protein-misfolding diseases: getting out of shape
-
Dobson C.M. Protein-misfolding diseases: getting out of shape. Nature 418 (2002) 729-730
-
(2002)
Nature
, vol.418
, pp. 729-730
-
-
Dobson, C.M.1
-
31
-
-
0347357617
-
Protein folding and misfolding
-
Dobson C.M. Protein folding and misfolding. Nature 426 (2003) 884-890
-
(2003)
Nature
, vol.426
, pp. 884-890
-
-
Dobson, C.M.1
-
32
-
-
71349087420
-
The generic nature of protein folding and misfolding
-
Atassi M.Z. (Ed), Springer
-
Dobson C.M. The generic nature of protein folding and misfolding. In: Atassi M.Z. (Ed). Protein Reviews (2006), Springer 21-41
-
(2006)
Protein Reviews
, pp. 21-41
-
-
Dobson, C.M.1
-
33
-
-
0031616362
-
Protein disorder and the evolution of molecular recognition: theory, predictions and observations
-
Dunker A.K., Garner E., Guilliot S., Romero P., Albercht K., Hart J., Obradovic Z., Kissinger C., and Villafranca J.E. Protein disorder and the evolution of molecular recognition: theory, predictions and observations. Pac. Symp. Biocomput. 3 (1998) 473-484
-
(1998)
Pac. Symp. Biocomput.
, vol.3
, pp. 473-484
-
-
Dunker, A.K.1
Garner, E.2
Guilliot, S.3
Romero, P.4
Albercht, K.5
Hart, J.6
Obradovic, Z.7
Kissinger, C.8
Villafranca, J.E.9
-
34
-
-
52249085709
-
Unnfoldomics decade: an update on intrinsically disordered proteins
-
Dunker A.K., Oldfield C.J., Meng.F J., Romero P., Yang J.Y., Chen J.W., Vacic V., Obradovic Z., and Uversky V.N. Unnfoldomics decade: an update on intrinsically disordered proteins. BMC Genomics 16 Suppl. 2 (2008) S1
-
(2008)
BMC Genomics
, vol.16
, Issue.SUPPL. 2
-
-
Dunker, A.K.1
Oldfield, C.J.2
Meng.F, J.3
Romero, P.4
Yang, J.Y.5
Chen, J.W.6
Vacic, V.7
Obradovic, Z.8
Uversky, V.N.9
-
35
-
-
0025105161
-
A point mutation of the rhodopsin gene in one form of retinitis pigmentosa
-
Dryja T.P., McGee T.L., Reichel E., Hahn L.B., Cowley G.S., Yandell D.W., Sandberg M.A., and Berson E.L. A point mutation of the rhodopsin gene in one form of retinitis pigmentosa. Nature 343 (1990) 364-366
-
(1990)
Nature
, vol.343
, pp. 364-366
-
-
Dryja, T.P.1
McGee, T.L.2
Reichel, E.3
Hahn, L.B.4
Cowley, G.S.5
Yandell, D.W.6
Sandberg, M.A.7
Berson, E.L.8
-
36
-
-
58149506229
-
Crystallin proteins and amyloid fibrils
-
Ecroyd H., and Carver J.A. Crystallin proteins and amyloid fibrils. Cell. Mol. Life Sci. 66 (2009) 62-81
-
(2009)
Cell. Mol. Life Sci.
, vol.66
, pp. 62-81
-
-
Ecroyd, H.1
Carver, J.A.2
-
37
-
-
0035846548
-
Molecular chaperones: inside and outside the Anfinsen cage
-
Ellis R.J. Molecular chaperones: inside and outside the Anfinsen cage. Curr. Biol. 11 (2001) R1038-R1040
-
(2001)
Curr. Biol.
, vol.11
-
-
Ellis, R.J.1
-
38
-
-
0035253217
-
Macromolecular crowding: an important but neglected aspect of the intracellular environment
-
Ellis R.J. Macromolecular crowding: an important but neglected aspect of the intracellular environment. Curr. Opin. Struct. Biol. 11 (2001) 114-119
-
(2001)
Curr. Opin. Struct. Biol.
, vol.11
, pp. 114-119
-
-
Ellis, R.J.1
-
39
-
-
0041822089
-
Join the crowd
-
Ellis R.J., and Minton A.P. Join the crowd. Nature 425 (2003) 27-28
-
(2003)
Nature
, vol.425
, pp. 27-28
-
-
Ellis, R.J.1
Minton, A.P.2
-
40
-
-
33947535828
-
Mechanisms involved in the protection of UV-induced protein inactivation by the corneal crystallin ALDH3A1
-
Estey T., Cantore M., Weston P.A., Carpenter J.F., Petrash J.M., and Vasiliou V. Mechanisms involved in the protection of UV-induced protein inactivation by the corneal crystallin ALDH3A1. J. Biol. Chem. 282 (2007) 4382-4392
-
(2007)
J. Biol. Chem.
, vol.282
, pp. 4382-4392
-
-
Estey, T.1
Cantore, M.2
Weston, P.A.3
Carpenter, J.F.4
Petrash, J.M.5
Vasiliou, V.6
-
41
-
-
68549104191
-
Nanotechnologies and controlled release systems for the delivery of antisense oligonucleotides and small interfering RNA
-
Fattal E., and Barratt G. Nanotechnologies and controlled release systems for the delivery of antisense oligonucleotides and small interfering RNA. Br. J. Pharmacol. 157 (2009) 179-194
-
(2009)
Br. J. Pharmacol.
, vol.157
, pp. 179-194
-
-
Fattal, E.1
Barratt, G.2
-
42
-
-
0034704752
-
A Drosophila model of Parkinson's disease
-
Feany M.B., and Bender W.W. A Drosophila model of Parkinson's disease. Nature 404 (2000) 394-398
-
(2000)
Nature
, vol.404
, pp. 394-398
-
-
Feany, M.B.1
Bender, W.W.2
-
43
-
-
0028889120
-
Contribution of cotranslational folding to the rate of formation of native protein structure
-
Fedorov N., and Baldwin T.O. Contribution of cotranslational folding to the rate of formation of native protein structure. Proc. Natl. Acad. Sci. U.S.A. 92 (1995) 1227-1231
-
(1995)
Proc. Natl. Acad. Sci. U.S.A.
, vol.92
, pp. 1227-1231
-
-
Fedorov, N.1
Baldwin, T.O.2
-
44
-
-
0037975647
-
Structural defects and the diagnosis of amyloidogenic propensity
-
Fernandez A., Kardos J., Scott L.R., Goto Y., and Berry R.S. Structural defects and the diagnosis of amyloidogenic propensity. Proc. Natl. Acad. Sci. U.S.A. 100 (2003) 6446-6451
-
(2003)
Proc. Natl. Acad. Sci. U.S.A.
, vol.100
, pp. 6446-6451
-
-
Fernandez, A.1
Kardos, J.2
Scott, L.R.3
Goto, Y.4
Berry, R.S.5
-
45
-
-
34548812551
-
The role of amyloid beta peptide 42 in Alzheimer's disease
-
Findeis M.A. The role of amyloid beta peptide 42 in Alzheimer's disease. Pharmacol. Ther. 116 (2007) 266-286
-
(2007)
Pharmacol. Ther.
, vol.116
, pp. 266-286
-
-
Findeis, M.A.1
-
47
-
-
13844255387
-
Natively unfolded proteins
-
Fink A.L. Natively unfolded proteins. Curr. Opin. Struct. Biol. 15 (2005) 35-41
-
(2005)
Curr. Opin. Struct. Biol.
, vol.15
, pp. 35-41
-
-
Fink, A.L.1
-
48
-
-
33749841522
-
The aggregation and fibrillation of alpha-synuclein
-
Fink A.L. The aggregation and fibrillation of alpha-synuclein. Acc. Chem. Res. 39 (2006) 628-634
-
(2006)
Acc. Chem. Res.
, vol.39
, pp. 628-634
-
-
Fink, A.L.1
-
49
-
-
14144250992
-
Contributions of hydrophobic domain interface interactions to the folding and stability of human gammaD-crystallin
-
Flaugh S.L., Kosinski-Collins M.S., and King J. Contributions of hydrophobic domain interface interactions to the folding and stability of human gammaD-crystallin. Protein Sci. 14 (2005) 569-581
-
(2005)
Protein Sci.
, vol.14
, pp. 569-581
-
-
Flaugh, S.L.1
Kosinski-Collins, M.S.2
King, J.3
-
51
-
-
65649111138
-
Liquid nitrogen cryotherapy for conjunctival amyloidosis
-
Fraunfelder F.W. Liquid nitrogen cryotherapy for conjunctival amyloidosis. Arch. Ophalmol. 127 (2009) 645-648
-
(2009)
Arch. Ophalmol.
, vol.127
, pp. 645-648
-
-
Fraunfelder, F.W.1
-
52
-
-
0029985732
-
Oxidative stress increases production of beta-amyloid precursor protein and beta-amyloid (Abeta) in mammalian lenses, and Abeta has toxic effects on lens epithelial cells
-
Frederikse P.H., Garland D., Zigler Jr. J.S., and Piatigorsky J. Oxidative stress increases production of beta-amyloid precursor protein and beta-amyloid (Abeta) in mammalian lenses, and Abeta has toxic effects on lens epithelial cells. J. Biol. Chem. 271 (1996) 10169-10174
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 10169-10174
-
-
Frederikse, P.H.1
Garland, D.2
Zigler Jr., J.S.3
Piatigorsky, J.4
-
54
-
-
54449101793
-
Heat shock transcription factor 1-activating compounds suppress polyglutamine-induced neurodegeneration through induction of multiple molecular chaperones
-
Fujikake N., Nagai Y., Popiel H.A., Okamoto Y., Yamaguchi M., and Toda T. Heat shock transcription factor 1-activating compounds suppress polyglutamine-induced neurodegeneration through induction of multiple molecular chaperones. J. Biol. Chem. 283 (2008) 26188-26197
-
(2008)
J. Biol. Chem.
, vol.283
, pp. 26188-26197
-
-
Fujikake, N.1
Nagai, Y.2
Popiel, H.A.3
Okamoto, Y.4
Yamaguchi, M.5
Toda, T.6
-
55
-
-
0036174010
-
Alpha-synuclein is phosphorylated in synucleinopathy lesions
-
Fujiwara H., Hasegawa M., Dohmae N., Kawashima A., Masliah E., Goldberg M.S., Shen J., Takio K., and Iwatsubo T. Alpha-synuclein is phosphorylated in synucleinopathy lesions. Nat. Cell Biol. 4 (2002) 160-164
-
(2002)
Nat. Cell Biol.
, vol.4
, pp. 160-164
-
-
Fujiwara, H.1
Hasegawa, M.2
Dohmae, N.3
Kawashima, A.4
Masliah, E.5
Goldberg, M.S.6
Shen, J.7
Takio, K.8
Iwatsubo, T.9
-
56
-
-
0035504258
-
Unfolding and refolding of a quinone oxidoreductase: α-crystallin, a molecular chaperone, assists its reactivation
-
Goenka S., Raman B., Ramakrishna T., and Rao C.M. Unfolding and refolding of a quinone oxidoreductase: α-crystallin, a molecular chaperone, assists its reactivation. Biochem. J. 359 (2001) 547-556
-
(2001)
Biochem. J.
, vol.359
, pp. 547-556
-
-
Goenka, S.1
Raman, B.2
Ramakrishna, T.3
Rao, C.M.4
-
57
-
-
0346727127
-
Protein degradation and protection against misfolded or damaged proteins
-
Goldberg A.L. Protein degradation and protection against misfolded or damaged proteins. Nature 426 (2003) 895-899
-
(2003)
Nature
, vol.426
, pp. 895-899
-
-
Goldberg, A.L.1
-
58
-
-
33750998186
-
Mutant myocilin nonsecretion in vivo is not sufficient to cause glaucoma
-
Gould D.B., Reedy M., Wilson L.A., Smith R.S., Johnson R.L., and John S.W.M. Mutant myocilin nonsecretion in vivo is not sufficient to cause glaucoma. Mol. Cell. Biol. 26 (2006) 8427-8436
-
(2006)
Mol. Cell. Biol.
, vol.26
, pp. 8427-8436
-
-
Gould, D.B.1
Reedy, M.2
Wilson, L.A.3
Smith, R.S.4
Johnson, R.L.5
John, S.W.M.6
-
59
-
-
0032941652
-
Cataract mutations and lens development
-
Graw J. Cataract mutations and lens development. Prog. Retin. Eye Res. 18 (1999) 235-267
-
(1999)
Prog. Retin. Eye Res.
, vol.18
, pp. 235-267
-
-
Graw, J.1
-
60
-
-
11144298645
-
Congenital hereditary cataracts
-
Graw J. Congenital hereditary cataracts. Int. J. Dev. Biol. 48 (2004) 1031-1044
-
(2004)
Int. J. Dev. Biol.
, vol.48
, pp. 1031-1044
-
-
Graw, J.1
-
61
-
-
61849122908
-
Genetics of crystallins: cataract and beyond
-
Graw J. Genetics of crystallins: cataract and beyond. Exp. Eye Res. 88 (2009) 173-189
-
(2009)
Exp. Eye Res.
, vol.88
, pp. 173-189
-
-
Graw, J.1
-
62
-
-
33748593902
-
Abnormal prion accumulation associated with retinal pathology in experimentally inoculated scrapie-affected sheep
-
Greenlee J.J., Hamir A.N., and West Greenlee M.H. Abnormal prion accumulation associated with retinal pathology in experimentally inoculated scrapie-affected sheep. Vet. Pathol. 43 (2006) 733-739
-
(2006)
Vet. Pathol.
, vol.43
, pp. 733-739
-
-
Greenlee, J.J.1
Hamir, A.N.2
West Greenlee, M.H.3
-
63
-
-
34548076604
-
Targeting amyloid-beta in glaucoma treatment
-
Guo L., Salt T.E., Luong V., Wood N., Cheung W., Maass A., Ferrari G., Russo-Marie F., Sillito A.M., Cheetham M.E., Moss S.E., Fitzke F.W., and Cordeiro M.F. Targeting amyloid-beta in glaucoma treatment. Proc. Natl. Acad. Sci. U.S.A. 104 (2007) 13444-13449
-
(2007)
Proc. Natl. Acad. Sci. U.S.A.
, vol.104
, pp. 13444-13449
-
-
Guo, L.1
Salt, T.E.2
Luong, V.3
Wood, N.4
Cheung, W.5
Maass, A.6
Ferrari, G.7
Russo-Marie, F.8
Sillito, A.M.9
Cheetham, M.E.10
Moss, S.E.11
Fitzke, F.W.12
Cordeiro, M.F.13
-
64
-
-
0030695478
-
Pathways of ubiquitin conjugation
-
Guo L., Salt T.E., Luong V., Wood N., Cheung W., Maass A., Ferrari G., Russo-Marie F., Sillito A.M., Haas A.L., and Siepman T.J. Pathways of ubiquitin conjugation. FASEB J. 11 (1997) 1257-1268
-
(1997)
FASEB J.
, vol.11
, pp. 1257-1268
-
-
Guo, L.1
Salt, T.E.2
Luong, V.3
Wood, N.4
Cheung, W.5
Maass, A.6
Ferrari, G.7
Russo-Marie, F.8
Sillito, A.M.9
Haas, A.L.10
Siepman, T.J.11
-
65
-
-
0036750801
-
Amyloid deposition in ocular tissues of patients with familial amyloidotic polyneuropathy (FAP)
-
Haraoka K., Ando Y., Ando E., Sandgren O., Hirata A., Nakamura M., Terazaki H., Tajiri T., Tanoue Y., Sun X., Okabe H., and Tanihara H. Amyloid deposition in ocular tissues of patients with familial amyloidotic polyneuropathy (FAP). Amyloid 9 (2002) 183-189
-
(2002)
Amyloid
, vol.9
, pp. 183-189
-
-
Haraoka, K.1
Ando, Y.2
Ando, E.3
Sandgren, O.4
Hirata, A.5
Nakamura, M.6
Terazaki, H.7
Tajiri, T.8
Tanoue, Y.9
Sun, X.10
Okabe, H.11
Tanihara, H.12
-
66
-
-
0015376691
-
Conformational changes in human lens proteins in cataract
-
Harding J.J. Conformational changes in human lens proteins in cataract. Biochem. J. 129 (1972) 97-100
-
(1972)
Biochem. J.
, vol.129
, pp. 97-100
-
-
Harding, J.J.1
-
67
-
-
0036597985
-
Viewing molecular mechanisms of ageing through a lens
-
Harding J.J. Viewing molecular mechanisms of ageing through a lens. Ageing Res. Rev. 1 (2002) 465-479
-
(2002)
Ageing Res. Rev.
, vol.1
, pp. 465-479
-
-
Harding, J.J.1
-
68
-
-
67049087108
-
Role of amyloid-beta glycine 33 in oligomerization, toxicity, and neuronal plasticity
-
Harmeier A., Wozny C., Rost B.R., Munter L.M., Hua H., Georgiev O., Beyermann M., Hildebrand P.W., Weise C., Schaffner W., Schmitz D., and Multhaup G. Role of amyloid-beta glycine 33 in oligomerization, toxicity, and neuronal plasticity. J. Neurosci. 29 (2009) 7582-7590
-
(2009)
J. Neurosci.
, vol.29
, pp. 7582-7590
-
-
Harmeier, A.1
Wozny, C.2
Rost, B.R.3
Munter, L.M.4
Hua, H.5
Georgiev, O.6
Beyermann, M.7
Hildebrand, P.W.8
Weise, C.9
Schaffner, W.10
Schmitz, D.11
Multhaup, G.12
-
69
-
-
0035823499
-
The molecular chaperone α-crystallin, inhibits amyloid formation by apolipoprotein C-II
-
Hatters D.M., Lindner R.A., Carver J.A., and Howlett G.J. The molecular chaperone α-crystallin, inhibits amyloid formation by apolipoprotein C-II. J. Biol. Chem. 276 (2001) 33755-33761
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 33755-33761
-
-
Hatters, D.M.1
Lindner, R.A.2
Carver, J.A.3
Howlett, G.J.4
-
70
-
-
0037247871
-
Prion protein accumulation in eyes of patients with sporadic and variant Creutzfeldt-Jakob disease
-
Head M.W., Northcott V., Rennison K., Ritchie D., McCardle L., Bunn T.J., McLennan N.F., Ironside J.W., Tullo A.B., and Bonshek R.E. Prion protein accumulation in eyes of patients with sporadic and variant Creutzfeldt-Jakob disease. Invest. Ophthalmol. Vis. Sci. 44 (2003) 342-346
-
(2003)
Invest. Ophthalmol. Vis. Sci.
, vol.44
, pp. 342-346
-
-
Head, M.W.1
Northcott, V.2
Rennison, K.3
Ritchie, D.4
McCardle, L.5
Bunn, T.J.6
McLennan, N.F.7
Ironside, J.W.8
Tullo, A.B.9
Bonshek, R.E.10
-
71
-
-
24044500298
-
Abnormal prion protein in the retina of the most commonly occurring subtype of sporadic Creutzfeldt-Jakob disease
-
Head M.W., Peden A.H., Yull H.M., Ritchie D.L., Bonshek R.E., Tullo A.B., and Ironside J.W. Abnormal prion protein in the retina of the most commonly occurring subtype of sporadic Creutzfeldt-Jakob disease. Br. J. Ophthalmol. 89 (2005) 1131-1133
-
(2005)
Br. J. Ophthalmol.
, vol.89
, pp. 1131-1133
-
-
Head, M.W.1
Peden, A.H.2
Yull, H.M.3
Ritchie, D.L.4
Bonshek, R.E.5
Tullo, A.B.6
Ironside, J.W.7
-
72
-
-
0019351880
-
Progressive retinal degeneration in scrapie-infected hamsters: a light and electron microscopic analysis
-
Hogan R.N., Baringer J.R., and Prusiner S.B. Progressive retinal degeneration in scrapie-infected hamsters: a light and electron microscopic analysis. Lab. Invest. 44 (1981) 34-42
-
(1981)
Lab. Invest.
, vol.44
, pp. 34-42
-
-
Hogan, R.N.1
Baringer, J.R.2
Prusiner, S.B.3
-
73
-
-
52149087029
-
Identification and localization of α-synuclein in human cornea
-
Hong S., Lee H.K., Kim C.Y., and Seong G.J. Identification and localization of α-synuclein in human cornea. Korean J. Ophthalmol. 22 (2008) 145-146
-
(2008)
Korean J. Ophthalmol.
, vol.22
, pp. 145-146
-
-
Hong, S.1
Lee, H.K.2
Kim, C.Y.3
Seong, G.J.4
-
74
-
-
48649101750
-
Suppression of keratoepithelin and myocilin by small interfering RNA
-
Huang A.J.W. Suppression of keratoepithelin and myocilin by small interfering RNA. Trans. Am. Ophthalmol. Soc. 105 (2007) 365-378
-
(2007)
Trans. Am. Ophthalmol. Soc.
, vol.105
, pp. 365-378
-
-
Huang, A.J.W.1
-
75
-
-
0028305304
-
A role for destabilizing amino acid replacements in light-chain amyloidosis
-
Hurle M.R., Helms L.R., Li L., Chan W., and Wetzel R. A role for destabilizing amino acid replacements in light-chain amyloidosis. Proc. Natl. Acad. Sci. U.S.A. 91 (1994) 5446-5450
-
(1994)
Proc. Natl. Acad. Sci. U.S.A.
, vol.91
, pp. 5446-5450
-
-
Hurle, M.R.1
Helms, L.R.2
Li, L.3
Chan, W.4
Wetzel, R.5
-
76
-
-
0037072934
-
A rhodopsin mutant linked to autosomal dominant retinitis pigmentosa is prone to aggregate and interacts with the ubiquitin proteasome system
-
Illing M.E., Rajan R.S., Bence N.F., and Kopito R.R. A rhodopsin mutant linked to autosomal dominant retinitis pigmentosa is prone to aggregate and interacts with the ubiquitin proteasome system. J. Biol. Chem. 277 (2002) 34150-34160
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 34150-34160
-
-
Illing, M.E.1
Rajan, R.S.2
Bence, N.F.3
Kopito, R.R.4
-
77
-
-
0035862866
-
Non-secretion of mutant proteins of the glaucoma gene myocilin in cultured TM cells and in aqueous humor
-
Jacobson N., Andrews M., Shepard A.R., Nishimura D., Searby C., Fingert J.H., Hageman G., Mullins R., Davidson B.L., Kwon Y.H., Alward W.L., Stone E.M., Clark A.F., and Sheffield V.C. Non-secretion of mutant proteins of the glaucoma gene myocilin in cultured TM cells and in aqueous humor. Hum. Mol. Genet. 10 (2001) 117-125
-
(2001)
Hum. Mol. Genet.
, vol.10
, pp. 117-125
-
-
Jacobson, N.1
Andrews, M.2
Shepard, A.R.3
Nishimura, D.4
Searby, C.5
Fingert, J.H.6
Hageman, G.7
Mullins, R.8
Davidson, B.L.9
Kwon, Y.H.10
Alward, W.L.11
Stone, E.M.12
Clark, A.F.13
Sheffield, V.C.14
-
78
-
-
0035167113
-
Lens crystallins and their microbial homologs: structure, stability and function
-
Jaenicke R., and Slingsby C. Lens crystallins and their microbial homologs: structure, stability and function. Crit. Rev. Biochem. Mol. Biol. 36 (2001) 435-499
-
(2001)
Crit. Rev. Biochem. Mol. Biol.
, vol.36
, pp. 435-499
-
-
Jaenicke, R.1
Slingsby, C.2
-
79
-
-
0032576605
-
Aggresomes: a cellular response to misfolded proteins
-
Johnston J.A., Ward C.L., and Kopito R.R. Aggresomes: a cellular response to misfolded proteins. J. Cell Biol. 143 (1998) 1883-1898
-
(1998)
J. Cell Biol.
, vol.143
, pp. 1883-1898
-
-
Johnston, J.A.1
Ward, C.L.2
Kopito, R.R.3
-
80
-
-
65249160170
-
The structure of the cataract-causing P23T mutant of human gammaD-crystallin exhibits distinctive local conformational and dynamic changes
-
Jung J., Byeon I.J., Wang Y., King J., and Gronenborn A.M. The structure of the cataract-causing P23T mutant of human gammaD-crystallin exhibits distinctive local conformational and dynamic changes. Biochemistry 48 (2009) 2597-2609
-
(2009)
Biochemistry
, vol.48
, pp. 2597-2609
-
-
Jung, J.1
Byeon, I.J.2
Wang, Y.3
King, J.4
Gronenborn, A.M.5
-
81
-
-
4043144280
-
Proteomic analysis of the soluble fraction from human corneal fibroblasts with reference to ocular transparency
-
Karring H., Thøgersen I.B., Klintworth G.K., Enghild J.J., and Møller-Pedersen T. Proteomic analysis of the soluble fraction from human corneal fibroblasts with reference to ocular transparency. Mol. Cell. Proteomics 3 (2004) 660-674
-
(2004)
Mol. Cell. Proteomics
, vol.3
, pp. 660-674
-
-
Karring, H.1
Thøgersen, I.B.2
Klintworth, G.K.3
Enghild, J.J.4
Møller-Pedersen, T.5
-
82
-
-
0028287273
-
Structure and function in rhodopsin. 7. Point mutations associated with autosomal dominant retinitis pigmentosa
-
Kaushal S., and Khorana H.G. Structure and function in rhodopsin. 7. Point mutations associated with autosomal dominant retinitis pigmentosa. Biochemistry 33 (1994) 6121-6128
-
(1994)
Biochemistry
, vol.33
, pp. 6121-6128
-
-
Kaushal, S.1
Khorana, H.G.2
-
83
-
-
12244256129
-
A case of vitreous amyloidosis without systemic symptoms in familial amyloidotic polyneuropathy
-
Kawaji T., Ando Y., Ando E., Nakamura M., Hirata A., and Tanihara H.H. A case of vitreous amyloidosis without systemic symptoms in familial amyloidotic polyneuropathy. Amyloid 11 (2004) 257-259
-
(2004)
Amyloid
, vol.11
, pp. 257-259
-
-
Kawaji, T.1
Ando, Y.2
Ando, E.3
Nakamura, M.4
Hirata, A.5
Tanihara, H.H.6
-
84
-
-
0033106510
-
Amyloid and Pro501 Thr-mutated (beta)ig-h3 gene product colocalize in lattice corneal dystrophy type III
-
Kawasaki S., Nishida K., Quantock A.J., Dota A., Bennett K., and Kinoshita S. Amyloid and Pro501 Thr-mutated (beta)ig-h3 gene product colocalize in lattice corneal dystrophy type III. Am. J. Ophthalmol. 127 (1999) 456-458
-
(1999)
Am. J. Ophthalmol.
, vol.127
, pp. 456-458
-
-
Kawasaki, S.1
Nishida, K.2
Quantock, A.J.3
Dota, A.4
Bennett, K.5
Kinoshita, S.6
-
85
-
-
36348929457
-
Orally administered amyloidophilic compound is effective in prolonging the incubation periods of animals cerebrally infected with prion diseases in a prion strain-dependent manner
-
Kawasaki Y., Kawagoe K., Chen C., Teruya K., Sakasegawa Y., and Doh-ura K. Orally administered amyloidophilic compound is effective in prolonging the incubation periods of animals cerebrally infected with prion diseases in a prion strain-dependent manner. J. Virol. 81 (2007) 12889-12898
-
(2007)
J. Virol.
, vol.81
, pp. 12889-12898
-
-
Kawasaki, Y.1
Kawagoe, K.2
Chen, C.3
Teruya, K.4
Sakasegawa, Y.5
Doh-ura, K.6
-
86
-
-
34648834051
-
Prion protein expression differences in microglia and astroglia influence scrapie-induced neurodegeneration in the retina and brain of transgenic mice
-
Kercher L., Favara C., Striebel J.F., LaCasse R., and Chesebro B. Prion protein expression differences in microglia and astroglia influence scrapie-induced neurodegeneration in the retina and brain of transgenic mice. J. Virol. 81 (2007) 10340-10351
-
(2007)
J. Virol.
, vol.81
, pp. 10340-10351
-
-
Kercher, L.1
Favara, C.2
Striebel, J.F.3
LaCasse, R.4
Chesebro, B.5
-
87
-
-
0028053692
-
Ocular amyloid deposition in familial amyloidosis finnish: an analysis of native and variant gelsolin in Meretoja's syndrome
-
Kivelä T., Tarkkanen A., Frangione B., Ghiso J., and Haltia M. Ocular amyloid deposition in familial amyloidosis finnish: an analysis of native and variant gelsolin in Meretoja's syndrome. Invest. Ophthalmol. Vis. Sci. 35 (1994) 3759-3769
-
(1994)
Invest. Ophthalmol. Vis. Sci.
, vol.35
, pp. 3759-3769
-
-
Kivelä, T.1
Tarkkanen, A.2
Frangione, B.3
Ghiso, J.4
Haltia, M.5
-
88
-
-
68149124522
-
Chaperone-like antibodies in neurodegenerative tauopathies: implication for immunotherapy
-
Kontsekova E., Ivanovova N., Handzusova M., and Novak M. Chaperone-like antibodies in neurodegenerative tauopathies: implication for immunotherapy. Cell. Mol. Neurobiol. 29 (2009) 793-798
-
(2009)
Cell. Mol. Neurobiol.
, vol.29
, pp. 793-798
-
-
Kontsekova, E.1
Ivanovova, N.2
Handzusova, M.3
Novak, M.4
-
89
-
-
0034578389
-
Aggresomes, inclusion bodies and protein aggregation
-
Kopito R.R. Aggresomes, inclusion bodies and protein aggregation. Trends Cell. Biol. 10 (2000) 524-530
-
(2000)
Trends Cell. Biol.
, vol.10
, pp. 524-530
-
-
Kopito, R.R.1
-
91
-
-
0039788641
-
On the role of kerato-epithelin in the pathogenesis of 5q31-linked corneal dystrophies
-
Korvatska E., Munier F.L., Chaubert P., Wang M.X., Mashima Y., Yamada M., Uffer S., Zografos L., and Schorderet D.F. On the role of kerato-epithelin in the pathogenesis of 5q31-linked corneal dystrophies. Invest. Ophthalmol. Vis. Sci. 40 (1999) 2213-2219
-
(1999)
Invest. Ophthalmol. Vis. Sci.
, vol.40
, pp. 2213-2219
-
-
Korvatska, E.1
Munier, F.L.2
Chaubert, P.3
Wang, M.X.4
Mashima, Y.5
Yamada, M.6
Uffer, S.7
Zografos, L.8
Schorderet, D.F.9
-
93
-
-
0037372175
-
In vitro unfolding, refolding, and polymerization of human γD crystallin, a protein involved in cataract formation
-
Kosinski-Collins M.S., and King J. In vitro unfolding, refolding, and polymerization of human γD crystallin, a protein involved in cataract formation. Protein Sci. 12 (2003) 12480-12490
-
(2003)
Protein Sci.
, vol.12
, pp. 12480-12490
-
-
Kosinski-Collins, M.S.1
King, J.2
-
94
-
-
0026047846
-
Nonuniform size distribution of nascent globin peptides, evidence for pause localization sites, and a cotranslational protein-folding model
-
Krasheninnikov I.A., Komar A.A., and Adzhubei I.A. Nonuniform size distribution of nascent globin peptides, evidence for pause localization sites, and a cotranslational protein-folding model. J. Protein Chem. 10 (1991) 445-453
-
(1991)
J. Protein Chem.
, vol.10
, pp. 445-453
-
-
Krasheninnikov, I.A.1
Komar, A.A.2
Adzhubei, I.A.3
-
95
-
-
33748136058
-
Periocular and orbital amyloidosis: clinical characteristics, management, and outcome
-
Leibovitch I., Selva D., Goldberg R.A., Sullivan T.J., Saeed P., Davis G., McCann J.D., McNab A., and Rootman J. Periocular and orbital amyloidosis: clinical characteristics, management, and outcome. Ophthalmology 113 (2006) 1657-1664
-
(2006)
Ophthalmology
, vol.113
, pp. 1657-1664
-
-
Leibovitch, I.1
Selva, D.2
Goldberg, R.A.3
Sullivan, T.J.4
Saeed, P.5
Davis, G.6
McCann, J.D.7
McNab, A.8
Rootman, J.9
-
96
-
-
69949084211
-
Protein aggregation as a paradigm of ageing
-
10.1016/j.bbagen.2009.06.005
-
Lindner A.B., and Demarez A. Protein aggregation as a paradigm of ageing. Biochim. Biophys. Acta (2009) 10.1016/j.bbagen.2009.06.005
-
(2009)
Biochim. Biophys. Acta
-
-
Lindner, A.B.1
Demarez, A.2
-
97
-
-
32444450909
-
Drusen deposits associated with aging and age-related macular degeneration contain nonfibrillar amyloid oligomers
-
Luibl V., Isas J.M., Kayed R., Glabe C.G., Langen R., and Chen J. Drusen deposits associated with aging and age-related macular degeneration contain nonfibrillar amyloid oligomers. J. Clin. Invest. 116 (2006) 378-385
-
(2006)
J. Clin. Invest.
, vol.116
, pp. 378-385
-
-
Luibl, V.1
Isas, J.M.2
Kayed, R.3
Glabe, C.G.4
Langen, R.5
Chen, J.6
-
98
-
-
2942718944
-
Reversal of mutant myocilin non-secretion and cell killing: implications for glaucoma
-
Liu Y., and Vollrath D. Reversal of mutant myocilin non-secretion and cell killing: implications for glaucoma. Hum. Mol. Genet. 13 (2004) 1193-1204
-
(2004)
Hum. Mol. Genet.
, vol.13
, pp. 1193-1204
-
-
Liu, Y.1
Vollrath, D.2
-
99
-
-
34250845054
-
α-Synuclein gene expression profile in the retina of vertebrates
-
Martínez-Navarrete G.C., Martín-Nieto J., Esteve-Rudd J., Angulo A., and Cuenca A.N. α-Synuclein gene expression profile in the retina of vertebrates. Mol. Vis. 13 (2007) 949-961
-
(2007)
Mol. Vis.
, vol.13
, pp. 949-961
-
-
Martínez-Navarrete, G.C.1
Martín-Nieto, J.2
Esteve-Rudd, J.3
Angulo, A.4
Cuenca, A.N.5
-
100
-
-
0028839438
-
Comparison of lethal and nonlethal transthyretin variants and their relationship to amyloid disease
-
McCutchen S.L., Lai Z., Miroi G.J., Kelly J.W., and Colon W. Comparison of lethal and nonlethal transthyretin variants and their relationship to amyloid disease. Biochemistry 34 (1995) 13527-13536
-
(1995)
Biochemistry
, vol.34
, pp. 13527-13536
-
-
McCutchen, S.L.1
Lai, Z.2
Miroi, G.J.3
Kelly, J.W.4
Colon, W.5
-
101
-
-
0036208082
-
Caspase activation and amyloid precursor protein cleavage in rat ocular hypertension
-
McKinnon S.J., Lehman D.M., Kerrigan-Baumrind L.A., Merges C.A., Pease M.E., Kerrigan D.F., Ransom N.L., Tahzib N.G., Reitsamer H.A., Levkovitch-Verbin H., Quigley H.A., and Zack D.J. Caspase activation and amyloid precursor protein cleavage in rat ocular hypertension. Invest. Ophthalmol. Vis. Sci. 43 (2002) 1077-1087
-
(2002)
Invest. Ophthalmol. Vis. Sci.
, vol.43
, pp. 1077-1087
-
-
McKinnon, S.J.1
Lehman, D.M.2
Kerrigan-Baumrind, L.A.3
Merges, C.A.4
Pease, M.E.5
Kerrigan, D.F.6
Ransom, N.L.7
Tahzib, N.G.8
Reitsamer, H.A.9
Levkovitch-Verbin, H.10
Quigley, H.A.11
Zack, D.J.12
-
102
-
-
0942276377
-
Amyloid fibril formation by lens crystallin proteins and its implications for cataract formation
-
Meehan S., Berry Y., Luisi B., Dobson C.M., Carver J.A., and MacPhee C.E. Amyloid fibril formation by lens crystallin proteins and its implications for cataract formation. J. Biol. Chem. 279 (2004) 3413-3419
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 3413-3419
-
-
Meehan, S.1
Berry, Y.2
Luisi, B.3
Dobson, C.M.4
Carver, J.A.5
MacPhee, C.E.6
-
103
-
-
17044363529
-
Mechanisms of cell death in rhodopsin retinitis pigmentosa: implications for therapy
-
Mendes H.F., van der Spuy J., Chapple J.P., and Cheetham M.E. Mechanisms of cell death in rhodopsin retinitis pigmentosa: implications for therapy. Trends Mol. Med. 11 (2005) 177-185
-
(2005)
Trends Mol. Med.
, vol.11
, pp. 177-185
-
-
Mendes, H.F.1
van der Spuy, J.2
Chapple, J.P.3
Cheetham, M.E.4
-
104
-
-
0023657520
-
Quasi-irreversibility in the unfolding-refolding transition of phosphoglycerate kinase induced by guanidine hydrochloride
-
Mitraki A., Betton J.M., Desmadril M., and Yon J.M. Quasi-irreversibility in the unfolding-refolding transition of phosphoglycerate kinase induced by guanidine hydrochloride. Eur. J. Biochem. 163 (1987) 29-34
-
(1987)
Eur. J. Biochem.
, vol.163
, pp. 29-34
-
-
Mitraki, A.1
Betton, J.M.2
Desmadril, M.3
Yon, J.M.4
-
105
-
-
44449119580
-
Noninvasive measurement of protein aggregation by mutant huntingtin fragments or α-synuclein in the lens
-
Muchowski P.J., Ramsden R., Nguyen Q.V., Arnett E.E., Greiling T.M., Anderson S.K., and Clark J.I. Noninvasive measurement of protein aggregation by mutant huntingtin fragments or α-synuclein in the lens. J. Biol. Chem. 283 (2008) 6330-6336
-
(2008)
J. Biol. Chem.
, vol.283
, pp. 6330-6336
-
-
Muchowski, P.J.1
Ramsden, R.2
Nguyen, Q.V.3
Arnett, E.E.4
Greiling, T.M.5
Anderson, S.K.6
Clark, J.I.7
-
106
-
-
0031020733
-
Kerato-epithelin mutations in four 5q31-linked corneal dystrophies
-
Munier F.L., Korvatska E., Djemai A., Le Paslier D., Zografos L., Pescia G., and Schorderet D.F. Kerato-epithelin mutations in four 5q31-linked corneal dystrophies. Nat. Genet. 15 (1997) 247-251
-
(1997)
Nat. Genet.
, vol.15
, pp. 247-251
-
-
Munier, F.L.1
Korvatska, E.2
Djemai, A.3
Le Paslier, D.4
Zografos, L.5
Pescia, G.6
Schorderet, D.F.7
-
107
-
-
67650620091
-
Amyloidosis-associated neurotrophic keratopathy precipitated by overcorrected blepharoptosis
-
Nguyen V.T., Hwang T.N., Shamie N., Chuck R.S., and McCulley T.J. Amyloidosis-associated neurotrophic keratopathy precipitated by overcorrected blepharoptosis. Cornea 28 (2009) 575-576
-
(2009)
Cornea
, vol.28
, pp. 575-576
-
-
Nguyen, V.T.1
Hwang, T.N.2
Shamie, N.3
Chuck, R.S.4
McCulley, T.J.5
-
108
-
-
36749045270
-
Early onset vitreous amyloidosis in familial amyloidotic polyneuropathy with a transthyretin Glu54Gly mutation is associated with elevated vitreous VEGF
-
O'Hearn T.M., Fawzi A., He S., Rao N.A., and Lim J.I. Early onset vitreous amyloidosis in familial amyloidotic polyneuropathy with a transthyretin Glu54Gly mutation is associated with elevated vitreous VEGF. Br. J. Ophthalmol. 91 (2007) 1607-1609
-
(2007)
Br. J. Ophthalmol.
, vol.91
, pp. 1607-1609
-
-
O'Hearn, T.M.1
Fawzi, A.2
He, S.3
Rao, N.A.4
Lim, J.I.5
-
109
-
-
38449111855
-
Formation of amyloid fibrils in vitro by human γD-crystallin and its isolated domains
-
Papanikolopoulou K., Mills-Henry I., Thol S.L., Wang Y., Gross A.A.R., Kirschner D.A., Decatur S.M., and King J. Formation of amyloid fibrils in vitro by human γD-crystallin and its isolated domains. Mol. Vis. 14 (2008) 81-89
-
(2008)
Mol. Vis.
, vol.14
, pp. 81-89
-
-
Papanikolopoulou, K.1
Mills-Henry, I.2
Thol, S.L.3
Wang, Y.4
Gross, A.A.R.5
Kirschner, D.A.6
Decatur, S.M.7
King, J.8
-
110
-
-
20444403757
-
Prediction of "aggregation-prone" and "aggregation-susceptible" regions in proteins associated with neurodegenerative diseases
-
Pawar A.P., Dubay K.F., Zurdo J., Chiti F., Vendruscolo M., and Dobson C.M. Prediction of "aggregation-prone" and "aggregation-susceptible" regions in proteins associated with neurodegenerative diseases. J. Mol. Biol. 350 (2005) 379-392
-
(2005)
J. Mol. Biol.
, vol.350
, pp. 379-392
-
-
Pawar, A.P.1
Dubay, K.F.2
Zurdo, J.3
Chiti, F.4
Vendruscolo, M.5
Dobson, C.M.6
-
111
-
-
34249663915
-
Insights into the beaded filament of the eye lens
-
Perng M.D., Zhang Q., and Quinlan R.A. Insights into the beaded filament of the eye lens. Exp. Cell Res. 313 (2007) 2180-2188
-
(2007)
Exp. Cell Res.
, vol.313
, pp. 2180-2188
-
-
Perng, M.D.1
Zhang, Q.2
Quinlan, R.A.3
-
112
-
-
0034602271
-
Interaction of human α-synuclein and Parkinson's disease variants with phospholipids: Structural analysis using site-directed mutagenesis
-
Perrin R.J., Woods W.S., Clayton D.F., and George J.M. Interaction of human α-synuclein and Parkinson's disease variants with phospholipids: Structural analysis using site-directed mutagenesis. J. Biol. Chem. 275 (2000) 34393-34398
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 34393-34398
-
-
Perrin, R.J.1
Woods, W.S.2
Clayton, D.F.3
George, J.M.4
-
113
-
-
67650410543
-
Biological and chemical approaches to diseases of proteostasis deficiency
-
Powers E.T., Morimoto R.I., Dillin A., Kelly J.W., and Balch W.E. Biological and chemical approaches to diseases of proteostasis deficiency. Annu. Rev. Biochem. 78 (2009) 959-991
-
(2009)
Annu. Rev. Biochem.
, vol.78
, pp. 959-991
-
-
Powers, E.T.1
Morimoto, R.I.2
Dillin, A.3
Kelly, J.W.4
Balch, W.E.5
-
114
-
-
0023063602
-
Prions causing degenerative neurological diseases
-
Prusiner S.B. Prions causing degenerative neurological diseases. Annu. Rev. Med. 38 (1987) 381-398
-
(1987)
Annu. Rev. Med.
, vol.38
, pp. 381-398
-
-
Prusiner, S.B.1
-
115
-
-
66049133683
-
Aging: central role for autophagy and the lysosomal degradative system
-
Rajawat Y.S., Hilioti Z., and Bossis I. Aging: central role for autophagy and the lysosomal degradative system. Ageing Res. Rev. 8 (2009) 199-213
-
(2009)
Ageing Res. Rev.
, vol.8
, pp. 199-213
-
-
Rajawat, Y.S.1
Hilioti, Z.2
Bossis, I.3
-
116
-
-
69949175897
-
Autophagy in neurodegeneration: fire-fighter and/or incendiarist?
-
Rami A. Autophagy in neurodegeneration: fire-fighter and/or incendiarist?. Neuropathol. Appl. Neurobiol. (2009)
-
(2009)
Neuropathol. Appl. Neurobiol.
-
-
Rami, A.1
-
117
-
-
33747160829
-
Cell based screening of inhibitors of transthyretin aggregation
-
Reixach N., Adamski-Werner S.L., Kelly J.W., Koziol J., and Buxbaum J.N. Cell based screening of inhibitors of transthyretin aggregation. Biochem. Biophys. Res. Commun. 348 (2006) 889-897
-
(2006)
Biochem. Biophys. Res. Commun.
, vol.348
, pp. 889-897
-
-
Reixach, N.1
Adamski-Werner, S.L.2
Kelly, J.W.3
Koziol, J.4
Buxbaum, J.N.5
-
118
-
-
33645669165
-
Prediction of nucleating sequences from amyloidogenic propensities of tau-related peptides
-
Rojas Quijano F.A., Morrow D., Wise B.M., Brancia F.L., and Goux W.J. Prediction of nucleating sequences from amyloidogenic propensities of tau-related peptides. Biochemistry 45 (2006) 4638-4652
-
(2006)
Biochemistry
, vol.45
, pp. 4638-4652
-
-
Rojas Quijano, F.A.1
Morrow, D.2
Wise, B.M.3
Brancia, F.L.4
Goux, W.J.5
-
119
-
-
0028110523
-
Rhodopsin accumulation at abnormal sites in retinas of mice with a human P23H rhodopsin transgene
-
Roof D.J., Adamian M., and Hayes A. Rhodopsin accumulation at abnormal sites in retinas of mice with a human P23H rhodopsin transgene. Invest. Ophthalmol. Vis. Sci. 35 (1996) 4049-4062
-
(1996)
Invest. Ophthalmol. Vis. Sci.
, vol.35
, pp. 4049-4062
-
-
Roof, D.J.1
Adamian, M.2
Hayes, A.3
-
120
-
-
58049214009
-
Tau oligomerization: a role for tau aggregation intermediates linked to neurodegeneration
-
Sahara N., Maeda S., and Takashima A. Tau oligomerization: a role for tau aggregation intermediates linked to neurodegeneration. Curr. Alzheimer Res. 5 (2008) 591-598
-
(2008)
Curr. Alzheimer Res.
, vol.5
, pp. 591-598
-
-
Sahara, N.1
Maeda, S.2
Takashima, A.3
-
121
-
-
0037099080
-
The cellular fate of mutant rhodopsin: quality control, degradation and aggresome formation
-
Saliba R.S., Munro P.N., Luthert P.J., and Cheetham M.E. The cellular fate of mutant rhodopsin: quality control, degradation and aggresome formation. J. Cell. Sci. 115 (2002) 2907-2918
-
(2002)
J. Cell. Sci.
, vol.115
, pp. 2907-2918
-
-
Saliba, R.S.1
Munro, P.N.2
Luthert, P.J.3
Cheetham, M.E.4
-
122
-
-
18744404774
-
Altered aggregation properties of mutant gamma-crystallins cause inherited cataract
-
Sandilands A., Hutcheson A.M., Long H.A., Prescott A.R., Vrensen G., Löster J., Klopp N., Lutz R.B., Graw J., Masaki S., Dobson C.M., MacPhee C.E., and Quinlan R.A. Altered aggregation properties of mutant gamma-crystallins cause inherited cataract. EMBO J. 21 (2002) 6005-6014
-
(2002)
EMBO J.
, vol.21
, pp. 6005-6014
-
-
Sandilands, A.1
Hutcheson, A.M.2
Long, H.A.3
Prescott, A.R.4
Vrensen, G.5
Löster, J.6
Klopp, N.7
Lutz, R.B.8
Graw, J.9
Masaki, S.10
Dobson, C.M.11
MacPhee, C.E.12
Quinlan, R.A.13
-
123
-
-
9444229933
-
Inhibition of amyloid fibrillogenesis and toxicity by a peptide chaperone
-
Santhoshkumar P., and Sharma K.K. Inhibition of amyloid fibrillogenesis and toxicity by a peptide chaperone. Mol. Cell. Biochem. 267 (2004) 147-155
-
(2004)
Mol. Cell. Biochem.
, vol.267
, pp. 147-155
-
-
Santhoshkumar, P.1
Sharma, K.K.2
-
124
-
-
0347987853
-
Folding proteins in fatal ways
-
Selkoe D.J. Folding proteins in fatal ways. Nature 426 (2003) 900-904
-
(2003)
Nature
, vol.426
, pp. 900-904
-
-
Selkoe, D.J.1
-
125
-
-
0034769477
-
Removal of oxidatively damaged proteins from lens cells by the ubiquitin-proteasome pathway
-
Shang F., Nowell Jr. T.R., and Taylor A. Removal of oxidatively damaged proteins from lens cells by the ubiquitin-proteasome pathway. Exp. Eye Res. 73 (2001) 229-238
-
(2001)
Exp. Eye Res.
, vol.73
, pp. 229-238
-
-
Shang, F.1
Nowell Jr., T.R.2
Taylor, A.3
-
126
-
-
37349075401
-
Silencing gene therapy for mutant membrane, secretory, and lipid proteins in retinitis pigmentosa (RP)
-
Shinohara T., Mulhern M.L., and Madson C.J. Silencing gene therapy for mutant membrane, secretory, and lipid proteins in retinitis pigmentosa (RP). Med. Hypotheses 70 (2008) 378-380
-
(2008)
Med. Hypotheses
, vol.70
, pp. 378-380
-
-
Shinohara, T.1
Mulhern, M.L.2
Madson, C.J.3
-
127
-
-
0346096508
-
Quality control in the endoplasmic reticulum protein factory
-
Sitia R., and Braakman I. Quality control in the endoplasmic reticulum protein factory. Nature 426 (2003) 891-894
-
(2003)
Nature
, vol.426
, pp. 891-894
-
-
Sitia, R.1
Braakman, I.2
-
128
-
-
0035827318
-
Protein misfolding and disease; protein refolding and therapy
-
Soto C. Protein misfolding and disease; protein refolding and therapy. FEBS Lett. 498 (2001) 204-207
-
(2001)
FEBS Lett.
, vol.498
, pp. 204-207
-
-
Soto, C.1
-
129
-
-
0037264120
-
Unfolding the role of protein misfolding in neurodegenerative diseases
-
Soto C. Unfolding the role of protein misfolding in neurodegenerative diseases. Nat. Rev. Neurosci. 4 (2003) 49-60
-
(2003)
Nat. Rev. Neurosci.
, vol.4
, pp. 49-60
-
-
Soto, C.1
-
130
-
-
67651030654
-
Influence of conformational antibodies on dissociation of fibrillar amyloid beta (A beta 1-42) in vitro
-
Subramanian S., Madhavadas S., and Balasubramanian P. Influence of conformational antibodies on dissociation of fibrillar amyloid beta (A beta 1-42) in vitro. Indian J. Exp. Biol. 47 (2009) 309-313
-
(2009)
Indian J. Exp. Biol.
, vol.47
, pp. 309-313
-
-
Subramanian, S.1
Madhavadas, S.2
Balasubramanian, P.3
-
131
-
-
0029922245
-
The crystal structure of transthyretin from chicken
-
Sunde M., Richardson S.J., Chang L., Pettersson T.M., Schreiber G., and Blake C.C. The crystal structure of transthyretin from chicken. Eur. J. Biochem. 236 (1996) 491-499
-
(1996)
Eur. J. Biochem.
, vol.236
, pp. 491-499
-
-
Sunde, M.1
Richardson, S.J.2
Chang, L.3
Pettersson, T.M.4
Schreiber, G.5
Blake, C.C.6
-
132
-
-
0027452148
-
Rhodopsin mutations responsible for autosomal dominant retinitis pigmentosa clustering of functional classes along the polypeptide chain
-
Sung C.H., Davenport C.M., and Nathans J. Rhodopsin mutations responsible for autosomal dominant retinitis pigmentosa clustering of functional classes along the polypeptide chain. J. Biol. Chem. 268 (1993) 26645-26649
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 26645-26649
-
-
Sung, C.H.1
Davenport, C.M.2
Nathans, J.3
-
133
-
-
0036221254
-
Synucleins in glaucoma: implication of γ-synuclein in glaucomatous alterations in the optic nerve
-
Surgucheva I., McMahan B., Ahmed F., Tomarev S., Wax M.B., and Surguchov A. Synucleins in glaucoma: implication of γ-synuclein in glaucomatous alterations in the optic nerve. J. Neurosci. Res. 68 (2002) 97-106
-
(2002)
J. Neurosci. Res.
, vol.68
, pp. 97-106
-
-
Surgucheva, I.1
McMahan, B.2
Ahmed, F.3
Tomarev, S.4
Wax, M.B.5
Surguchov, A.6
-
134
-
-
31544470611
-
Protein aggregation in retinal cells and approaches to cell protection
-
Surgucheva I., Ninkina N., Buchman V.L., Grasing K., and Surguchov A. Protein aggregation in retinal cells and approaches to cell protection. Cell. Mol. Neurobiol. 25 (2005) 1051-1066
-
(2005)
Cell. Mol. Neurobiol.
, vol.25
, pp. 1051-1066
-
-
Surgucheva, I.1
Ninkina, N.2
Buchman, V.L.3
Grasing, K.4
Surguchov, A.5
-
135
-
-
31544462086
-
Interaction of myocilin with gamma-synuclein affects its secretion and aggregation
-
Surgucheva I., Park B.C., Yue B.Y., Tomarev S., and Surguchov A. Interaction of myocilin with gamma-synuclein affects its secretion and aggregation. Cell. Mol. Neurobiol. 25 (2005) 1009-1033
-
(2005)
Cell. Mol. Neurobiol.
, vol.25
, pp. 1009-1033
-
-
Surgucheva, I.1
Park, B.C.2
Yue, B.Y.3
Tomarev, S.4
Surguchov, A.5
-
136
-
-
57149084065
-
Molecular and cellular biology of synucleins
-
Surguchov A. Molecular and cellular biology of synucleins. Int. Rev. Cytol. Cell Biol. 270 (2008) 225-317
-
(2008)
Int. Rev. Cytol. Cell Biol.
, vol.270
, pp. 225-317
-
-
Surguchov, A.1
-
138
-
-
67650602950
-
Keratoconus associated with corneal stromal amyloid deposition containing TGFBIp
-
Tai T.Y., Damani M.R., Vo R., Rayner S.A., Glasgow B.J., Hofbauer J.D., Casey R., and Aldave A.J. Keratoconus associated with corneal stromal amyloid deposition containing TGFBIp. Cornea 28 (2009) 589-593
-
(2009)
Cornea
, vol.28
, pp. 589-593
-
-
Tai, T.Y.1
Damani, M.R.2
Vo, R.3
Rayner, S.A.4
Glasgow, B.J.5
Hofbauer, J.D.6
Casey, R.7
Aldave, A.J.8
-
139
-
-
0042819915
-
Intrinsically unstructured proteins evolve by repeat expansion
-
Tompa P. Intrinsically unstructured proteins evolve by repeat expansion. BioEssays 25 (2003) 847-855
-
(2003)
BioEssays
, vol.25
, pp. 847-855
-
-
Tompa, P.1
-
140
-
-
0026625426
-
Complete rescue of photoreceptor dysplasia and degeneration in transgenic retinal degeneration slow (rds) mice
-
Travis G.H., Groshan K.R., Lloyd M., and Bok D. Complete rescue of photoreceptor dysplasia and degeneration in transgenic retinal degeneration slow (rds) mice. Neuron 9 (1992) 113-119
-
(1992)
Neuron
, vol.9
, pp. 113-119
-
-
Travis, G.H.1
Groshan, K.R.2
Lloyd, M.3
Bok, D.4
-
141
-
-
85019814382
-
Eye lens proteins and cataracts
-
Fink A.L., and Uversky V.N. (Eds), Springer
-
Truscott R.J.W. Eye lens proteins and cataracts. In: Fink A.L., and Uversky V.N. (Eds). Protein Misfolding, Aggregation and Conformational Disease, Part B vol. 6 (2007), Springer 435-447
-
(2007)
Protein Misfolding, Aggregation and Conformational Disease, Part B
, vol.6
, pp. 435-447
-
-
Truscott, R.J.W.1
-
142
-
-
0036128797
-
Natively unfolded proteins: a point where biology waits for physics
-
Uversky V.N. Natively unfolded proteins: a point where biology waits for physics. Protein Sci. 11 (2002) 739-756
-
(2002)
Protein Sci.
, vol.11
, pp. 739-756
-
-
Uversky, V.N.1
-
143
-
-
0141861067
-
Protein folding revisited A polypeptided chain at the folding-misfolding-non-folding cross-roads: which way to go?
-
Uversky V.N. Protein folding revisited A polypeptided chain at the folding-misfolding-non-folding cross-roads: which way to go?. Cell. Mol. Life Sci. 60 (2003) 1852-1871
-
(2003)
Cell. Mol. Life Sci.
, vol.60
, pp. 1852-1871
-
-
Uversky, V.N.1
-
144
-
-
45449091418
-
Amyloidogenesis of naturally unfolded proteins
-
Uversky V.N. Amyloidogenesis of naturally unfolded proteins. Curr. Alzheimer's Res. 5 (2008) 260-267
-
(2008)
Curr. Alzheimer's Res.
, vol.5
, pp. 260-267
-
-
Uversky, V.N.1
-
145
-
-
2342569618
-
Conformational constraints for amyloid fibrillation: the importance of being unfolded
-
Uversky V.N., and Fink A.L. Conformational constraints for amyloid fibrillation: the importance of being unfolded. Biochim. Biophys. Acta 1698 (2004) 131-153
-
(2004)
Biochim. Biophys. Acta
, vol.1698
, pp. 131-153
-
-
Uversky, V.N.1
Fink, A.L.2
-
146
-
-
0034669882
-
Why are "natively unfolded" proteins unstructured under physiologic conditions?
-
Uversky V.N., Gillespie J.R., and Fink A.L. Why are "natively unfolded" proteins unstructured under physiologic conditions?. Proteins 41 (2000) 415-427
-
(2000)
Proteins
, vol.41
, pp. 415-427
-
-
Uversky, V.N.1
Gillespie, J.R.2
Fink, A.L.3
-
147
-
-
0035816404
-
Pesticides directly accelerate the rate of alpha synuclein fibril formation: a possible factor in Parkinson's disease
-
Uversky V.N., Li J., and Fink A.L. Pesticides directly accelerate the rate of alpha synuclein fibril formation: a possible factor in Parkinson's disease. FEBS Lett. 500 (2001) 105-108
-
(2001)
FEBS Lett.
, vol.500
, pp. 105-108
-
-
Uversky, V.N.1
Li, J.2
Fink, A.L.3
-
148
-
-
41449104565
-
Prediction of intrinsic disorder and its use in functional proteomics
-
Uversky V.N., Radivojac P., Iakoucheva L.M., Obradovic Z., and Dunker A.K. Prediction of intrinsic disorder and its use in functional proteomics. Methods Mol. Biol. 408 (2007) 69-92
-
(2007)
Methods Mol. Biol.
, vol.408
, pp. 69-92
-
-
Uversky, V.N.1
Radivojac, P.2
Iakoucheva, L.M.3
Obradovic, Z.4
Dunker, A.K.5
-
149
-
-
0036195521
-
Subepithelial corneal amyloid deposits in a case of congenital glaucoma
-
Vemuganti G.K., and Mandal A.K. Subepithelial corneal amyloid deposits in a case of congenital glaucoma. Cornea 21 (2002) 315-317
-
(2002)
Cornea
, vol.21
, pp. 315-317
-
-
Vemuganti, G.K.1
Mandal, A.K.2
-
150
-
-
0034458454
-
The cerebral proteopathies: neurodegenerative disorders of protein conformation and assembly
-
Walker L.C., and LeVine H. The cerebral proteopathies: neurodegenerative disorders of protein conformation and assembly. Mol. Neurobiol. 21 (2000) 83-95
-
(2000)
Mol. Neurobiol.
, vol.21
, pp. 83-95
-
-
Walker, L.C.1
LeVine, H.2
-
152
-
-
0028840915
-
Degradation of CFTR by the ubiquitin-proteasome pathway
-
Ward C.L., Omura S., and Kopito R.R. Degradation of CFTR by the ubiquitin-proteasome pathway. Cell 83 (1995) 121-127
-
(1995)
Cell
, vol.83
, pp. 121-127
-
-
Ward, C.L.1
Omura, S.2
Kopito, R.R.3
-
153
-
-
19944426695
-
Celastrols as inducers of the heat shock response and cytoprotection
-
Westerheide S.D., Bosman J.D., Mbadugha B.N., Kawahara T.L., Matsumoto G., Kim S., Gu W., Devlin J.P., Silverman R.B., and Morimoto R.I. Celastrols as inducers of the heat shock response and cytoprotection. J. Biol. Chem. 279 (2004) 56053-56060
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 56053-56060
-
-
Westerheide, S.D.1
Bosman, J.D.2
Mbadugha, B.N.3
Kawahara, T.L.4
Matsumoto, G.5
Kim, S.6
Gu, W.7
Devlin, J.P.8
Silverman, R.B.9
Morimoto, R.I.10
-
154
-
-
57449087203
-
Preventing β-amyloid fibrillization and deposition: β-sheet breakers and pathological chaperone inhibitors
-
Wisniewski T., and Sadowski M. Preventing β-amyloid fibrillization and deposition: β-sheet breakers and pathological chaperone inhibitors. BMC Neurosci. 9 Suppl. 2 (2008) S5
-
(2008)
BMC Neurosci.
, vol.9
, Issue.SUPPL. 2
-
-
Wisniewski, T.1
Sadowski, M.2
-
155
-
-
34248376062
-
Sodium 4-phenylbutyrate acts as a chemical chaperone on misfolded myocilin to rescue cells from endoplasmic reticulum stress and apoptosis
-
Yam G.H., Gaplovska-Kysela K., Zuber C., and Roth J. Sodium 4-phenylbutyrate acts as a chemical chaperone on misfolded myocilin to rescue cells from endoplasmic reticulum stress and apoptosis. Invest. Ophthalmol. Vis. Sci. 48 (2007) 1683-1690
-
(2007)
Invest. Ophthalmol. Vis. Sci.
, vol.48
, pp. 1683-1690
-
-
Yam, G.H.1
Gaplovska-Kysela, K.2
Zuber, C.3
Roth, J.4
-
156
-
-
18044398967
-
Vitreous fluid levels of beta-amyloid (1-42) and tau in patients with retinal diseases
-
Yoneda S., Hara H., Hirata A., Fukushima M., Inomata Y., and Tanihara H. Vitreous fluid levels of beta-amyloid (1-42) and tau in patients with retinal diseases. Jpn. J. Ophthalmol. 492 (2005) 106-108
-
(2005)
Jpn. J. Ophthalmol.
, vol.492
, pp. 106-108
-
-
Yoneda, S.1
Hara, H.2
Hirata, A.3
Fukushima, M.4
Inomata, Y.5
Tanihara, H.6
-
157
-
-
26444478610
-
The potential role of amyloid beta in the pathogenesis of age-related macular degeneration
-
Yoshida T., Ohno-Matsui K., Ichinose S., Sato T., Iwata N., Saido T.C., Hisatomi T., Mochizuki M., and Morita I. The potential role of amyloid beta in the pathogenesis of age-related macular degeneration. J. Clin. Invest. 115 (2005) 2793-2800
-
(2005)
J. Clin. Invest.
, vol.115
, pp. 2793-2800
-
-
Yoshida, T.1
Ohno-Matsui, K.2
Ichinose, S.3
Sato, T.4
Iwata, N.5
Saido, T.C.6
Hisatomi, T.7
Mochizuki, M.8
Morita, I.9
-
158
-
-
57649131080
-
Identification of the primary targets of carbamylation in bovine lens proteins by mass spectrometry
-
Zhang J., Yan H., Harding J.J., Liu Z.X., Wang X., and Ruan Y.S. Identification of the primary targets of carbamylation in bovine lens proteins by mass spectrometry. Curr. Eye Res. 33 (2008) 963-976
-
(2008)
Curr. Eye Res.
, vol.33
, pp. 963-976
-
-
Zhang, J.1
Yan, H.2
Harding, J.J.3
Liu, Z.X.4
Wang, X.5
Ruan, Y.S.6
-
159
-
-
0032013091
-
Transthyretin mutation (serine 84) associated with familial amyloid polyneuropathy in a Hungarian family
-
Zólyomi Z., Benson M.D., Halász K., Uemichi T., and Fekete G. Transthyretin mutation (serine 84) associated with familial amyloid polyneuropathy in a Hungarian family. Amyloid 5 (1998) 30-34
-
(1998)
Amyloid
, vol.5
, pp. 30-34
-
-
Zólyomi, Z.1
Benson, M.D.2
Halász, K.3
Uemichi, T.4
Fekete, G.5
|