Mitochondrial abnormalities in spinal and bulbar muscular atrophy

Human Molecular Genetics

Volumn 18, Issue 1, 2009, Pages 27-42

  Ranganathan, Srikanth ^a   Harmison, George G ^a   Meyertholen, Kristin ^a   Pennuto, Maria ^a   Burnett, Barrington G ^a   Fischbeck, Kenneth H ^a  

^a NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ANDROGEN RECEPTOR; CASPASE 3; CASPASE 9; CYCLOSPORIN A; DOXYCYCLINE; IDEBENONE; MANGANESE SUPEROXIDE DISMUTASE; MITOCHONDRIAL PERMEABILITY TRANSITION PORE; MITOCHONDRIAL PROTEIN; MUTANT PROTEIN; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1; POLYGLUTAMINE; PROTEIN BAX; REACTIVE OXYGEN METABOLITE; TRANSCRIPTION FACTOR; UBIDECARENONE; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANTIOXIDANT ACTIVITY; ARTICLE; BRAIN MITOCHONDRION; CELL CULTURE; CELL MEMBRANE DEPOLARIZATION; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GENE MUTATION; GENETIC TRANSCRIPTION; KENNEDY DISEASE; LIGAND BINDING; MITOCHONDRIAL MEMBRANE; MUTANT; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN EXPRESSION; RAT;

ANIMALIA; MUS;

EID: 57649207936     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddn310     Document Type: Article

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