Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)

Experimental Neurology

Volumn 200, Issue 1, 2006, Pages 8-18

  Katsuno, Masahisa ^a   Adachi, Hiroaki ^a   Waza, Masahiro ^a   Banno, Haruhiko ^a   Suzuki, Keisuke ^a   Tanaka, Fumiaki ^a   Doyu, Manabu ^a   Sobue, Gen ^a  

^a NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

17 Allylamino geldanamycin; Androgen receptor; Axonal transport; Geranylgeranylacetone; Heat shock protein; Histone deacetylase inhibitor; Luteinizing hormone releasing hormone analog; Polyglutamine; Spinal and bulbar muscular atrophy; Testosterone

Indexed keywords

FLUTAMIDE; HEAT SHOCK PROTEIN 90; LEUPRORELIN; TESTOSTERONE;

ANDROGEN THERAPY; BRAIN STEM; CLINICAL FEATURE; EXON; GENE MUTATION; HISTOPATHOLOGY; HUMAN; KENNEDY DISEASE; MOLECULAR DYNAMICS; MOTONEURON; NONHUMAN; PATHOGENESIS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; REVIEW; SKIN BIOPSY; SPINAL CORD VENTRAL HORN;

ANIMALS; DISEASE MODELS, ANIMAL; HEAT-SHOCK PROTEINS; HORMONE ANTAGONISTS; HUMANS; MUSCULAR ATROPHY, SPINAL;

EID: 33746077664     PISSN: 00144886     EISSN: 10902430     Source Type: Journal    
DOI: 10.1016/j.expneurol.2006.01.021     Document Type: Review

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