Mitochondrial ATP synthase disorders: Molecular mechanisms and the quest for curative therapeutic approaches

Biochimica et Biophysica Acta - Molecular Cell Research

Volumn 1793, Issue 1, 2009, Pages 186-199

  Kucharczyk, Roza ^a   Zick, Michael ^b   Bietenhader, Maïlis ^a   Rak, Malgorzata ^a   Couplan, Elodie ^c,d,e,f   Blondel, Marc ^c,d,e,f   Caubet, Stéphane Duvezin ^a   di Rago, Jean Paul ^a  

^a Institut de Biochimie et Genetique Cellulaires   (France)

^b UNIVERSITY OF MUNICH   (Germany)

^c INSERM   (France)

^d FACULTÉ DE MÉDECINE ET DES SCIENCES DE LA SANTÉ   (France)

^e ETABLISSEMENT FRANÇAIS DU SANG   (France)

^f CHU MORVAN   (France)

Author keywords

ATP synthase; Drug screening; Mitochondrial biogenesis; Mitochondrial diseases; NARP and MILS syndromes; Yeast

Indexed keywords

CELL NUCLEUS DNA; MITOCHONDRIAL DNA; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ANALYSIS; GENE MUTATION; HUMAN; NEUROMUSCULAR DISEASE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN FUNCTION; REVIEW;

MAMMALIA;

EID: 56349168862     PISSN: 01674889     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbamcr.2008.06.012     Document Type: Review

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