Subcomplexes of human ATP synthase mark mitochondrial biosynthesis disorders

Annals of Neurology

Volumn 59, Issue 2, 2006, Pages 265-275

  Carrozzo, Rosalba ^a   Wittig, Ilka ^b   Santorelli, Filippo M ^a   Bertini, Enrico ^a   Hofmann, Sabine ^c   Brandt, Ulrich ^b   Schägger, Hermann ^b,d  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^b GOETHE UNIVERSITY   (Germany)

^c Klinikum Schwabing   (Germany)

^d UNIVERSITY HOSPITAL FRANKFURT   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; FLAVINE ADENINE NUCLEOTIDE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; TRANSFER RNA; UBIQUINOL CYTOCHROME C REDUCTASE;

ARTICLE; ATP6 GENE; ENERGY CONSUMPTION; GENE; GENE MUTATION; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE; MOLECULAR GENETICS; NEUROMUSCULAR DISEASE; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DOMAIN; RESPIRATORY CHAIN;

BINDING SITES; BIOLOGICAL MARKERS; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX III; ELECTROPHORESIS, GEL, TWO-DIMENSIONAL; ELECTROPHORESIS, POLYACRYLAMIDE GEL; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MITOCHONDRIAL PROTON-TRANSLOCATING ATPASES; NEUROBLASTOMA; PROTEIN CONFORMATION; SUBMITOCHONDRIAL PARTICLES; TUMOR CELLS, CULTURED;

EID: 32044475420     PISSN: 03645134     EISSN: None     Source Type: Journal    
DOI: 10.1002/ana.20729     Document Type: Article

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