Mitochondrial threshold effects

Biochemical Journal

Volumn 370, Issue 3, 2003, Pages 751-762

  Rossignol, Rodrigue ^a   Faustin, Benjamin ^a   Rocher, Christophe ^a   Malgat, Monique ^a   Mazat, Jean Pierre ^a   Letellier, Thierry ^a  

^a INSERM   (France)

Author keywords

Complementation; Metabolic Control Analysis; Mitochondrial diseases; Mitochondrial DNA; Oxidative phosphorylation; Threshold effect

Indexed keywords

CELLS; DNA; PROTEINS;

GENETIC DEFECTS;

DISEASES;

ADENOSINE TRIPHOSPHATE; CARRIER PROTEIN; CYTOCHROME C OXIDASE; MESSENGER RNA; MITOCHONDRIAL DNA; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); TRANSFER RNA; UBIQUINOL CYTOCHROME C REDUCTASE;

CELL ACTIVITY; CELL GROWTH; CELL LINE; CLINICAL FEATURE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENERGY METABOLISM; ENZYME ACTIVITY; ENZYME KINETICS; ENZYME SUBUNIT; EXTERNAL OPHTHALMOPLEGIA; GENE DELETION; GENE EXPRESSION; GENE MUTATION; GENETIC DISORDER; GENETIC TRANSCRIPTION; GENETIC VARIABILITY; GLYCOLYSIS; HETEROPLASMY; HOMOPLASY; HUMAN; LIVER MITOCHONDRION; MELAS SYNDROME; MERRF SYNDROME; METABOLIC REGULATION; MITOCHONDRIAL RESPIRATION; MUSCLE MITOCHONDRION; MUTANT; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PHENOTYPE; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN SYNTHESIS; QUANTITATIVE ANALYSIS; RESPIRATORY CHAIN; REVIEW; RNA TRANSLATION; TRANSLATION REGULATION; WILD TYPE;

ANIMALS; CELL LINE; DNA, MITOCHONDRIAL; ENERGY METABOLISM; GENE EXPRESSION REGULATION; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MUTATION; OXIDATIVE PHOSPHORYLATION; PHENOTYPE;

EID: 0037444769     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/BJ20021594     Document Type: Review

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