Structure, functioning, and assembly of the ATP synthase in cells from patients with the T8993G mitochondrial DNA mutation. Comparison with the enzyme in Rho cells completely lacking mtDNA

Journal of Biological Chemistry

Volumn 275, Issue 15, 2000, Pages 11075-11081

  García, José J ^b,c   Ogilvie, Isla ^b   Robinson, Brian H ^a   Capaldi, Roderick A ^b  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b UNIVERSITY OF OREGON   (United States)

^c MCGILL UNIVERSITY   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

MITOCHONDRIAL DNA; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

ARTICLE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; ENZYME ANALYSIS; ENZYME ISOLATION; ENZYME PURIFICATION; ENZYME STRUCTURE; FIBROBLAST; HUMAN; HUMAN CELL; MUTATION; PRIORITY JOURNAL;

ADENOSINE TRIPHOSPHATE; BLOTTING, WESTERN; CATALYSIS; CELL LINE; DNA, MITOCHONDRIAL; ENZYME STABILITY; HUMANS; MEMBRANE POTENTIALS; MITOCHONDRIA; MUTATION; PROTON-TRANSLOCATING ATPASES;

EID: 0034646642     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.275.15.11075     Document Type: Article

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