Disease-associated mutations in CIAS1 induce cathepsin B-dependent rapid cell death of human THP-1 monocytic cells

Blood

Volumn 109, Issue 7, 2007, Pages 2903-2911

  Fujisawa, Akihiro ^a   Kambe, Naotomo ^a   Saito, Megumu ^a   Nishikomori, Ryuta ^a   Tanizaki, Hideaki ^a   Kanazawa, Nobuo ^a,b   Adachi, Souichi ^a   Heike, Toshio ^a   Sagara, Junji ^c   Suda, Takashi ^d   Nakahata, Tatsutoshi ^a   Miyachi, Yoshiki ^a  

^a KYOTO UNIVERSITY   (Japan)

^b WAKAYAMA MEDICAL UNIVERSITY   (Japan)

^c SHINSHU UNIVERSITY   (Japan)

^d KANAZAWA UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CATHEPSIN B; CRYOPYRIN; IMIQUIMOD; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN; INTERLEUKIN 1BETA CONVERTING ENZYME; LACTATE DEHYDROGENASE; UNCLASSIFIED DRUG;

APOPTOSIS; ARTICLE; AUTOINFLAMMATORY DISEASE; CELL DEATH; CINCA SYNDROME; COLD INDUCED AUTOINFLAMMATORY SYNDROME 1 GENE; DISEASE ASSOCIATION; DRUG MECHANISM; ENZYME RELEASE; FAMILIAL COLD AUTOINFLAMMATORY SYNDROME; GENE; GENE MUTATION; GENETIC ASSOCIATION; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; LEUKEMIA CELL; MEMBRANE DAMAGE; MONOCYTE; MUCKLE WELLS SYNDROME; MYELOID LEUKEMIA; PRIORITY JOURNAL;

EID: 33947596456     PISSN: 00064971     EISSN: 00064971     Source Type: Journal    
DOI: 10.1182/blood-2006-07-033597     Document Type: Article

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