Insights into the molecular basis of polyglutamine neurodegeneration from studies of a spinocerebellar ataxia type 7 mouse model

Cytogenetic and Genome Research

Volumn 100, Issue 1-4, 2003, Pages 164-174

  Grote, S K ^a   La Spada, A R ^a  

^a UNIVERSITY OF WASHINGTON MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GENE PRODUCT; POLYGLUTAMINE;

ADENO ASSOCIATED VIRUS; BRAIN STEM; CELL AGGREGATION; CLINICAL FEATURE; GENE EXPRESSION; GENETIC MANIPULATION; HISTOPATHOLOGY; HUMAN; IMMUNOHISTOCHEMISTRY; MOLECULAR BIOLOGY; NERVE DEGENERATION; NEUROTOXICITY; NONHUMAN; NUCLEOTIDE REPEAT; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; RETINA DEGENERATION; REVIEW; SPINOCEREBELLAR DEGENERATION; TRANSCRIPTION REGULATION; VIRAL GENE DELIVERY SYSTEM;

BRAIN STEM; DISEASE MODELS, ANIMAL; HEREDODEGENERATIVE DISORDERS, NERVOUS SYSTEM; NERVE TISSUE PROTEINS; PEPTIDES; RETINAL DEGENERATION; SPINOCEREBELLAR ATAXIAS; TRINUCLEOTIDE REPEAT EXPANSION;

ATAXIA;

EID: 0344531461     PISSN: 14248581     EISSN: None     Source Type: Journal    
DOI: 10.1159/000072851     Document Type: Review

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