Glutamine repeats and neurodegeneration

Annual Review of Neuroscience

Volumn 23, Issue , 2000, Pages 217-247

  Zoghbi, Huda Y ^a   Orr, Harry T ^b  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF MINNESOTA   (United States)

Author keywords

DRPLA; Huntington disease; Nuclear inclusions; Polyglutamine diseases; Protein aggregates; SBMA; SCA; Triplet repeat; Ubiquitin

Indexed keywords

GENE PRODUCT; GLUTAMINE;

DENTATORUBROPALLIDOLUYSIAN ATROPHY; GENE EXPRESSION; GENE MUTATION; HUNTINGTON CHOREA; MOUSE; MUSCLE ATROPHY; NERVE DEGENERATION; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; REVIEW; SPINOCEREBELLAR DEGENERATION; TRINUCLEOTIDE REPEAT;

ANIMALS; GLUTAMINE; HUMANS; HUNTINGTON DISEASE; MUSCULAR DISORDERS, ATROPHIC; NEURODEGENERATIVE DISEASES; PEPTIDES; REPETITIVE SEQUENCES, AMINO ACID; SPINOCEREBELLAR ATAXIAS;

EID: 0034094873     PISSN: 0147006X     EISSN: None     Source Type: Book Series    
DOI: 10.1146/annurev.neuro.23.1.217     Document Type: Review

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