Similarities between spinocerebellar ataxia type 7 (SCA7) cell models and human brain: Proteins recruited in inclusions and activation of caspase-3

Human Molecular Genetics

Volumn 10, Issue 22, 2001, Pages 2569-2579

  Zander, C ^a,b   Takahashi, J ^a,c   El Hachimi, K H ^a   Fujigasaki, H ^a   Albanese, V ^a   Lebre, A S ^a   Stevanin, G ^a   Duyckaerts, C ^a   Brice, A ^a,d  

^a PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^b KAROLINSKA INSTITUTE   (Sweden)

^c JIKEI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^d STANFORD UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 7; CASPASE 3; HEAT SHOCK PROTEIN; MUTANT PROTEIN; POLYGLUTAMINE; PROTEASOME; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

ADULT; ARTICLE; AUTOPHAGY; AUTOSOMAL DOMINANT DISORDER; BLINDNESS; BRAIN; BRAIN CORTEX; BRAIN TISSUE; CELL CULTURE; CELL INCLUSION; CELL LINE; CELL NUCLEUS; CEREBELLAR ATAXIA; CONTROLLED STUDY; DENSE BODY; DISEASE COURSE; ELECTRON; GENE ACTIVITY; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; HUMAN TISSUE; MECHANICS; NERVE CELL NECROSIS; NEUROBLASTOMA CELL; PRIORITY JOURNAL; PROTEIN FOLDING; SCHOOL CHILD; SPINOCEREBELLAR DEGENERATION; STRESS;

ATAXIA;

EID: 0035888620     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/10.22.2569     Document Type: Article

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