Expanded polyglutamines induce neurodegeneration and trans-neuronal alterations in cerebellum and retina of SCA7 transgenic mice

Human Molecular Genetics

Volumn 9, Issue 17, 2000, Pages 2491-2506

  Yvert, Gaël ^a   Lindenberg, Katrin S ^b,c   Picaud, Serge ^d   Landwehrmeyer, G Bernhard ^b,c   Sahel, José Alain ^d   Mandel, Jean Louis ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^b UNIVERSITY OF FREIBURG   (Germany)

^c UNIVERSITY OF ULM   (Germany)

^d INSERM   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 7; CELL PROTEIN; CHAPERONE; POLYGLUTAMINE; PROTEASOME; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CEREBELLAR ATAXIA; CEREBELLUM; CHO CELL; CONTROLLED STUDY; DEGENERATIVE DISEASE; GENE EXPRESSION REGULATION; GENE MUTATION; GENETIC LINKAGE; MOUSE; NERVE DEGENERATION; NEUROTOXICITY; NONHUMAN; PATHOGENESIS; PHOTORECEPTOR; POSTSYNAPTIC MEMBRANE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PURKINJE CELL; RETINA; RETINA ROD; SYNAPSE; TISSUE DISTRIBUTION; TRANSGENIC MOUSE; VISUOMOTOR COORDINATION;

ANIMALIA; ATAXIA; MUS MUSCULUS;

EID: 0034641891     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/9.17.2491     Document Type: Article

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