Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1

Nature Genetics

Volumn 19, Issue 2, 1998, Pages 148-154

  Cummings, Christopher J ^a   Mancini, Michael A ^a   Antalffy, Barbara ^a   DeFranco, Donald B ^c   Orr, Harry T ^d   Zoghbi, Huda Y ^a,b  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b HOWARD HUGHES MEDICAL INSTITUTE   (United States)

^c UNIVERSITY OF PITTSBURGH   (United States)

^d UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHAPERONE; PROTEASOME;

ARTICLE; CELL NUCLEUS; CEREBELLAR ATAXIA; GENETIC TRANSFECTION; HELA CELL; HUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DNA BINDING; PROTEIN FOLDING; PROTEIN LOCALIZATION; TRANSGENIC MOUSE;

ATAXIA; MUS MUSCULUS;

EID: 0031838352     PISSN: 10614036     EISSN: None     Source Type: Journal    
DOI: 10.1038/502     Document Type: Article

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