Accumulated α-synuclein affects the progression of GM2 gangliosidoses

Experimental Neurology

Volumn 284, Issue , 2016, Pages 38-49

  Suzuki, Kyoko ^a   Yamaguchi, Akira ^a   Yamanaka, Shoji ^a   Kanzaki, Seiichi ^a   Kawashima, Masato ^a   Togo, Takashi ^a   Katsuse, Omi ^a   Koumitsu, Noriko ^a   Aoki, Naoya ^a   Iseki, Eizo ^b   Kosaka, Kenji ^a   Yamaguchi, Kayoko ^a   Hashimoto, Makoto ^c   Aoki, Ichiro ^a   Hirayasu, Yoshio ^a  

^a YOKOHAMA CITY UNIVERSITY   (Japan)

^b JUNTENDO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^c TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

Author keywords

Alpha synuclein; Autophagy; GM2 gangliosidoses; Manganese superoxide dismutase 2; Reactive oxygen species; Sandhoff disease

Indexed keywords

ALPHA SYNUCLEIN; GANGLIOSIDE GM2; MANGANESE SUPEROXIDE DISMUTASE; MESSENGER RNA; PROTEASOME; REACTIVE OXYGEN METABOLITE; UBIQUITIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOPHAGY; BIOACCUMULATION; BRAIN MITOCHONDRION; CHILD; CONTROLLED STUDY; DOPAMINERGIC NERVE CELL; GENE DELETION; HUMAN; HUMAN TISSUE; LIPID PEROXIDATION; MALE; MICROGLIA; MOUSE; NERVE CELL DEGENERATION; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN EXPRESSION; SANDHOFF DISEASE;

EID: 84979623365     PISSN: 00144886     EISSN: 10902430     Source Type: Journal    
DOI: 10.1016/j.expneurol.2016.07.011     Document Type: Article

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