Apoptotic cell death in mouse models of G(M2) gangliosidosis and observations on human Tay-Sachs and Sandhoff diseases

Human Molecular Genetics

Volumn 6, Issue 11, 1997, Pages 1879-1885

  Huang, Jing Qi ^a   Trasler, Jacquetta M ^b   Igdoura, Suleiman ^a   Michaud, Jean ^c   Hanai, Nobuo ^d   Gravel, Roy A ^a  

^a RESEARCH INSTITUTE OF THE MCGILL UNIVERSITY HEALTH CENTRE   (Canada)

^b MCGILL UNIVERSITY   (Canada)

^c UNIVERSITY OF MONTREAL   (Canada)

^d KYOWA HAKKO KOGYO CO LTD   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

BETA N ACETYLHEXOSAMINIDASE A; BETA N ACETYLHEXOSAMINIDASE B;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; AUTOPSY; BRAIN; CELL DEATH; CENTRAL NERVOUS SYSTEM; DEGENERATIVE DISEASE; ENZYME SUBUNIT; GM2 GANGLIOSIDOSIS; HUMAN; HUMAN TISSUE; MOUSE; NERVE CELL NECROSIS; NONHUMAN; ONSET AGE; PRIORITY JOURNAL; SANDHOFF DISEASE; SPINAL CORD; TAY SACHS DISEASE;

EID: 0030782030     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/6.11.1879     Document Type: Article

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