Neuronal and glial accumulation of α- and β-synucleins in human lipidoses

Acta Neuropathologica

Volumn 114, Issue 5, 2007, Pages 481-489

  Suzuki, Kyoko ^a   Iseki, Eizo ^b   Togo, Takashi ^a   Yamaguchi, Akira ^a   Katsuse, Omi ^a   Katsuyama, Kayoko ^a   Kanzaki, Seiichi ^a   Shiozaki, Kazumasa ^a   Kawanishi, Chiaki ^a   Yamashita, Sumimasa ^a   Tanaka, Yukichi ^c   Yamanaka, Shoji ^a   Hirayasu, Yoshio ^a  

^a YOKOHAMA CITY UNIVERSITY   (Japan)

^b JUNTENDO TOKYO KOTO GERIATRIC MEDICAL CENTER   (Japan)

^c KANAGAWA CHILDREN'S MEDICAL CENTER   (Japan)

Author keywords

synuclein; Lipidstorage; Lysosome; Neuronal nuclei; Peroxisome

Indexed keywords

ALPHA SYNUCLEIN; BETA SYNUCLEIN; GLYCOLIPID; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; COHORT ANALYSIS; CONTROLLED STUDY; FEMALE; GALACTOSIALIDOSIS; GLIA CELL; HUMAN; HUMAN TISSUE; LIPID STORAGE; LIPIDOSIS; MALE; METACHROMATIC LEUKODYSTROPHY; NERVE CELL; PONS; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; SANDHOFF DISEASE; TAY SACHS DISEASE;

ADULT; ALPHA-SYNUCLEIN; ANTIGENS, NUCLEAR; BETA-SYNUCLEIN; BRAIN; BRAIN DISEASES, METABOLIC, INBORN; CHILD, PRESCHOOL; COHORT STUDIES; HUMANS; LIPID METABOLISM; LIPIDOSES; LYSOSOMAL STORAGE DISEASES, NERVOUS SYSTEM; MALE; MIDDLE AGED; NERVE TISSUE PROTEINS; NEUROGLIA; NEURONS; PEROXISOMAL DISORDERS; SANDHOFF DISEASE; SYNUCLEINS;

EID: 34948881759     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-007-0264-z     Document Type: Article

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