Nuclear lamina remodelling and its implications for human disease

Cell and Tissue Research

Volumn 360, Issue 3, 2015, Pages 621-631

  Chojnowski, Alexandre ^a   Ong, Peh Fern ^a   Dreesen, Oliver ^a  

^a INSTITUTE OF MEDICAL BIOLOGY   (Singapore)

Author keywords

Autosomal dominant leukodystrophy; Hutchinson Gilford progeria syndrome; Lamin A C; Lamin B1; Lamina remodelling; Laminopathies

Indexed keywords

CELL PROTEIN; LAMIN A; LAMIN B; LAMIN B1; LAMIN C; PROGERIN PROTEIN; PROTEOLIPID PROTEIN; UNCLASSIFIED DRUG; LAMIN;

ATAXIA TELANGIECTASIA; CANCER CELL; CELL AGING; CELL COMPOSITION; CELL DAMAGE; CELL DIFFERENTIATION; CELL INVASION; CELL PROLIFERATION; CELL REMODELLING; CELL STRUCTURE; CELLULAR DISTRIBUTION; DISEASE ASSOCIATION; DNA DAMAGE; DOWN REGULATION; EMBRYO DEVELOPMENT; GENE; GENE DUPLICATION; GENE LOCUS; GENETIC ASSOCIATION; HUMAN; LAMINOPATHY; LEUKODYSTROPHY; LMNA GENE; LMNB1 GENE; NONHUMAN; NUCLEAR LAMINA; NUCLEAR SHAPE; PHENOTYPE; PHYSICAL PARAMETERS; POINT MUTATION; PRIORITY JOURNAL; PROGERIA; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN PHOSPHORYLATION; REVIEW; T LYMPHOCYTE ACTIVATION; TELOMERE SHORTENING; TISSUE RIGIDITY; ANIMAL; DISEASES; GENETIC PREDISPOSITION; GENETICS; MUTATION; PATHOLOGY;

ANIMALS; CELL AGING; DISEASE; GENETIC PREDISPOSITION TO DISEASE; HUMANS; LAMINS; MUTATION; NUCLEAR LAMINA;

EID: 84930277396     PISSN: 0302766X     EISSN: 14320878     Source Type: Journal    
DOI: 10.1007/s00441-014-2069-4     Document Type: Review

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