Embryonic expression of the common progeroid lamin A splice mutation arrests postnatal skin development

Aging Cell

Volumn 13, Issue 2, 2014, Pages 292-302

  McKenna, Tomás ^a   Rosengardten, Ylva ^a   Viceconte, Nikenza ^a   Baek, Jean Ha ^a   Grochová, Diana ^a   Eriksson, Maria ^a  

^a KAROLINSKA INSTITUTE   (Sweden)

Author keywords

Aging; HGPS; Lamin B; Lamin B receptor; Progerin; Restrictive dermopathy

Indexed keywords

DNA; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN; LAMIN A; LAMIN B;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BASAL CELL; CELL DIFFERENTIATION; CONTROLLED STUDY; EMBRYO; EPIDERMIS; GAP JUNCTION; GENE EXPRESSION; GENE MUTATION; GENE OVEREXPRESSION; MOUSE; NONHUMAN; PHENOTYPE; POSTNATAL DEVELOPMENT; PRIORITY JOURNAL; PROTEIN EXPRESSION; SEBACEOUS GLAND; SIGNAL TRANSDUCTION; SKIN; SKIN EPITHELIUM; SKIN WATER LOSS; TIGHT JUNCTION; UPREGULATION;

ANIMALIA;

AGING; HGPS; LAMIN B; LAMIN B RECEPTOR; PROGERIN; RESTRICTIVE DERMOPATHY;

ANIMALS; ANIMALS, NEWBORN; BIOLOGICAL MARKERS; CELL DIFFERENTIATION; DIGESTIVE SYSTEM; EMBRYO, MAMMALIAN; EPIDERMIS; FEMALE; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HUMANS; INFLAMMATION; LAMIN TYPE A; LAMIN TYPE B; MICE; MICE, TRANSGENIC; MUTATION; NF-KAPPA B; PHENOTYPE; PROGERIA; RECEPTORS, CYTOPLASMIC AND NUCLEAR; RNA SPLICING; SIGNAL TRANSDUCTION; SKIN; TIGHT JUNCTIONS; UP-REGULATION; WATER LOSS, INSENSIBLE;

EID: 84895780946     PISSN: 14749718     EISSN: 14749726     Source Type: Journal    
DOI: 10.1111/acel.12173     Document Type: Article

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