Immunodetection of disease-associated conformers of mutant Cu/Zn superoxide dismutase 1 selectively expressed in degenerating neurons in amyotrophic lateral sclerosis

Journal of Neuropathology and Experimental Neurology

Volumn 72, Issue 7, 2013, Pages 646-661

  Sábado, Javier ^a   Casanovas, Anna ^a   Hernández, Sara ^a   Piedrafita, Lidia ^a   Hereu, Marta ^a   Esquerda, Josep E ^a  

^a UNIVERSITY OF LLEIDA   (Spain)

Author keywords

Amyotrophic lateral sclerosis; Conformational specific anti SOD1 antibody; Microglia; Motoneuron; Superoxide dismutase

Indexed keywords

AJ10 ANTIBODY; CELL PROTEIN; COPPER ZINC SUPEROXIDE DISMUTASE; ENHANCED GREEN FLUORESCENT PROTEIN; POLYCLONAL ANTIBODY; PURINERGIC P2X4 RECEPTOR; UBIQUITIN; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANTIBODY LABELING; ARTICLE; CROSS REACTION; GLIA CELL; HUMAN; HUMAN TISSUE; IMMUNODETECTION; IMMUNOGENICITY; IMMUNOHISTOCHEMISTRY; IMMUNOPRECIPITATION; IMMUNOREACTIVITY; MALE; MICROGLIA; MOTONEURON; MOUSE; MUTANT; MUTATION; NERVE CELL DEGENERATION; NERVOUS SYSTEM INFLAMMATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; SPINAL CORD; SPINAL CORD TRANSSECTION;

AGED; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; ANTIBODY SPECIFICITY; CELL LINE; DISEASE MODELS, ANIMAL; FEMALE; GENE EXPRESSION REGULATION; GREEN FLUORESCENT PROTEINS; HUMANS; MALE; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MUTATION; NERVE DEGENERATION; NERVE TISSUE PROTEINS; NEURONS; SPINAL CORD; SUPEROXIDE DISMUTASE;

EID: 84879944791     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e318297fd10     Document Type: Article

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