Complex I deficiencies in neurological disorders

Trends in Molecular Medicine

Volumn 19, Issue 1, 2013, Pages 61-69

  Papa, Sergio ^a,b   De Rasmo, Domenico ^a,b  

^a CNR   (Italy)

^b UNIVERSITY OF BARI   (Italy)

Author keywords

CAMP PKA signaling; Down syndrome; Mitochondrial biogenesis; Mitochondrial disease; Mitochondrial ROS balance; Neurological disorders; Parkinson disease; Respiratory complex I

Indexed keywords

CYCLIC AMP; HEAT SHOCK PROTEIN 70; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE KINASE; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; REACTIVE OXYGEN METABOLITE; SIRTUIN 1; SIRTUIN 3; SIRTUIN 4; SIRTUIN 5;

CHROMOSOME 21; COMPLEX I DEFICIENCY; CYCLIC AMP RESPONSIVE ELEMENT; DOWN SYNDROME; ENCEPHALOMYOPATHY; EXON; GENE DELETION; GENE EXPRESSION; GENE MUTATION; GENETIC DISORDER; HUMAN; MEMBRANE POTENTIAL; MUTATION; NEUROLOGIC DISEASE; NONHUMAN; PARKINSON DISEASE; PROTEIN BINDING; PROTEIN EXPRESSION; PROTEIN PHOSPHORYLATION; REVIEW;

CYCLIC AMP; DOWN SYNDROME; ELECTRON TRANSPORT COMPLEX I; HUMANS; MITOCHONDRIAL DISEASES; NERVOUS SYSTEM DISEASES; OXIDATIVE PHOSPHORYLATION; PARKINSON DISEASE; REACTIVE OXYGEN SPECIES;

EID: 84871717112     PISSN: 14714914     EISSN: 1471499X     Source Type: Journal    
DOI: 10.1016/j.molmed.2012.11.005     Document Type: Review

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