Mitochondrial complex III stabilizes complex I in the absence of NDUFS4 to provide partial activity

Human Molecular Genetics

Volumn 21, Issue 1, 2012, Pages 115-120

  Calvaruso, Maria Antonietta ^a   Willems, Peter ^b   Van den brand, Mariël ^a   Valsecchi, Federica ^b   Kruse, Shane ^c   Palmiter, Richard ^c   Smeitink, Jan ^a   Nijtmans, Leo ^a  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^c UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GENE PRODUCT; NICOTINAMIDE ADENINE DINUCLEOTIDE; PROTEIN NDUFS4; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; ELECTRON TRANSPORT; ENZYME STABILITY; FATALITY; GENE; GENE INACTIVATION; GENE MUTATION; KNOCKOUT MOUSE; MITOCHONDRIAL ENCEPHALOMYOPATHY; MOUSE; NDUFS4 GENE; NONHUMAN; PENETRANCE; PHENOTYPE; PRIORITY JOURNAL; PROTEIN PROTEIN INTERACTION; RESPIRATORY CHAIN;

ANIMALS; DISEASE MODELS, ANIMAL; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX III; HUMANS; MICE; MICE, KNOCKOUT; MITOCHONDRIA; MITOCHONDRIAL ENCEPHALOMYOPATHIES; PROTEIN BINDING; PROTEIN STABILITY;

EID: 83455169110     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr446     Document Type: Article

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