Mitochondrial bioenergetics and dynamics interplay in complex I-deficient fibroblasts

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1802, Issue 5, 2010, Pages 443-453

  Moran M ^a,c   Rivera, H ^a,c   Sanchez Arago ^b,c   Blazquez A ^a,c   Merinero, B ^b,c   Ugalde, C ^a,c   Arenas, J ^a,c   Cuezva, J M ^b,c   Martin M A ^a,c  

^a HOSPITAL UNIVERSITARIO 12 DE OCTUBRE   (Spain)

^b CSIC   (Spain)

^c CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED DE ENFERMEDADES RARAS CIBERER   (Spain)

Author keywords

Bioenergetics; Mitochondrial disease; Mitochondrial dynamics; NDUFA1; NDUFV1

Indexed keywords

CELL PROTEIN; DYNAMIN RELATED PROTEIN 1; MITOCHONDRIAL PROTEIN; MITOFUSIN 2; PROTEIN NDUFA1; PROTEIN NDUFV1; PROTEIN OPA1; REACTIVE OXYGEN METABOLITE; UNCLASSIFIED DRUG;

ARTICLE; BIOENERGY; CASE REPORT; CELL CULTURE; CHILD; COMPLEX I DEFICIENCY; CONTROLLED STUDY; FIBROBLAST; GENE MUTATION; GROWTH RATE; HUMAN; HUMAN CELL; INFANT; MALE; MITOCHONDRION; OXYGEN CONSUMPTION; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN EXPRESSION; SCHOOL CHILD;

ACIDOSIS; ADENOSINE TRIPHOSPHATE; BLOTTING, WESTERN; CELLS, CULTURED; ELECTRON TRANSPORT COMPLEX I; ENERGY METABOLISM; EPILEPSY; FIBROBLASTS; FLOW CYTOMETRY; FLUORESCENT ANTIBODY TECHNIQUE; GLYCOLYSIS; HUMANS; INFANT; LEUKOENCEPHALOPATHIES; MALE; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MUTATION; NADH DEHYDROGENASE; OXYGEN CONSUMPTION; REACTIVE OXYGEN SPECIES; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; SKIN;

EID: 77950371493     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbadis.2010.02.001     Document Type: Article

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