Understanding mitochondrial complex I assembly in health and disease

Biochimica et Biophysica Acta - Bioenergetics

Volumn 1817, Issue 6, 2012, Pages 851-862

  Mimaki, Masakazu ^a   Wang, Xiaonan ^a   McKenzie, Matthew ^b   Thorburn, David R ^c   Ryan, Michael T ^a  

^a LA TROBE UNIVERSITY   (Australia)

^b HUDSON INSTITUTE OF MEDICAL RESEARCH   (Australia)

^c UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

Assembly factor; Complex I; Complex I deficiency; Mitochondria; Respiratory chain

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ADENOSINE TRIPHOSPHATE; APOPTOSIS INDUCING FACTOR; CELL NUCLEUS DNA; MITOCHONDRIAL DNA; NUCLEOTIDE BINDING PROTEIN; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); TOLL LIKE RECEPTOR;

BIOGENESIS; CARDIOMYOPATHY; CHLAMYDOMONAS REINHARDTII; CHROMOSOME 20; CHROMOSOME 3; CHROMOSOME 6; COMPLEX I DEFICIENCY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ELECTRON TRANSPORT; ENZYME STRUCTURE; EUKARYOTIC CELL; GENE MUTATION; HUMAN; LEBER HEREDITARY OPTIC NEUROPATHY; LEIGH DISEASE; LEUKODYSTROPHY; MELAS SYNDROME; MITOCHONDRIAL ENCEPHALOPATHY; MITOCHONDRIAL MEMBRANE; NEUROSPORA CRASSA; NONHUMAN; OPEN READING FRAME; OXIDATIVE PHOSPHORYLATION; PHYLOGENY; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN FUNCTION; PROTEIN METHYLATION; RESPIRATORY CHAIN; REVIEW;

ACYL-COA DEHYDROGENASES; ANIMALS; ELECTRON TRANSPORT COMPLEX I; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MITOCHONDRIAL PROTEINS; NADH DEHYDROGENASE; OXIDATIVE PHOSPHORYLATION; PROTEIN MULTIMERIZATION; PROTEIN STRUCTURE, QUATERNARY; PROTEIN SUBUNITS;

BACTERIA (MICROORGANISMS); EUKARYOTA; MAMMALIA;

EID: 84860697620     PISSN: 00052728     EISSN: 18792650     Source Type: Journal    
DOI: 10.1016/j.bbabio.2011.08.010     Document Type: Review

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