TDP-43 and FUS/TLS: Cellular functions and implications for neurodegeneration

FEBS Journal

Volumn 278, Issue 19, 2011, Pages 3550-3568

  Fiesel, Fabienne C ^a   Kahle, Philipp J ^a  

^a UNIVERSITY OF TÜBINGEN   (Germany)

Author keywords

ALS; autophagy; FTLD; FUS; HDAC6; RNA; RNA metabolism; splicing; TDP 43; transcription

Indexed keywords

BINDING PROTEIN; FUSED IN SARCOMA PROTEIN; HISTONE DEACETYLASE 6; MESSENGER RNA; MICRORNA; TAR DNA BINDING PROTEIN; TRANSMEMBRANE CONDUCTANCE REGULATOR; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; AUTOPHAGY; CELL NUCLEUS INCLUSION BODY; FRONTOTEMPORAL DEMENTIA; HUMAN; MUTATOR GENE; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN RNA BINDING; REVIEW; RNA DEGRADATION; RNA PROCESSING; RNA SPLICING; RNA STABILITY; RNA TRANSLATION; RNA TRANSPORT;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AUTOPHAGY; CYTOPLASMIC GRANULES; DNA-BINDING PROTEINS; FRONTOTEMPORAL LOBAR DEGENERATION; GENE EXPRESSION REGULATION; HUMANS; NERVE DEGENERATION; RNA; RNA STABILITY; RNA-BINDING PROTEIN FUS;

EID: 80052968310     PISSN: 1742464X     EISSN: 17424658     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2011.08258.x     Document Type: Review

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