Pathological accumulation of atrophin-1 in dentatorubralpallidoluysian atrophy

International Journal of Clinical and Experimental Pathology

Volumn 4, Issue 4, 2011, Pages 378-384

  Suzuki, Yasuyo ^a   Yazawa, Ikuru ^a  

^a NATIONAL CENTER FOR GERIATRICS AND GERONTOLOGY   (Japan)

Author keywords

Atrophin 1 (ATN1); Dentatorubral pallidoluysian atrophy (DRPLA); Neurodegeneration; Polyglutamine (polyQ) disease

Indexed keywords

ATROPHIN 1; ATROPHIN-1; NERVE PROTEIN; PEPTIDE; POLYGLUTAMINE;

ANIMAL; CENTRAL NERVOUS SYSTEM; DISEASE MODEL; GENETIC PREDISPOSITION; GENETICS; HUMAN; METABOLISM; MUTATION; MYOCLONUS EPILEPSY; PATHOLOGY; PHENOTYPE; PROTEIN PROCESSING; REVIEW; UPREGULATION;

ANIMALS; CENTRAL NERVOUS SYSTEM; DISEASE MODELS, ANIMAL; GENETIC PREDISPOSITION TO DISEASE; HUMANS; MUTATION; MYOCLONIC EPILEPSIES, PROGRESSIVE; NERVE TISSUE PROTEINS; PEPTIDES; PHENOTYPE; PROTEIN PROCESSING, POST-TRANSLATIONAL; UP-REGULATION;

EID: 80051607553     PISSN: None     EISSN: 19362625     Source Type: Journal    
DOI: None     Document Type: Article

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