Proteolytic processing regulates pathological accumulation in dentatorubral-pallidoluysian atrophy

FEBS Journal

Volumn 277, Issue 23, 2010, Pages 4873-4887

  Suzuki, Yasuyo ^a   Nakayama, Kimiko ^a   Hashimoto, Naohiro ^a   Yazawa, Ikuru ^a  

^a NATIONAL CENTER FOR GERIATRICS AND GERONTOLOGY   (Japan)

Author keywords

Atrophin 1; Dentatorubral pallidoluysian atrophy; DRPLA; DRPLA protein; Neurodegeneration; Polyglutamine

Indexed keywords

ATROPHIN 1; CASPASE; POLYGLUTAMINE; REGULATOR PROTEIN; UNCLASSIFIED DRUG;

ARTICLE; CARBOXY TERMINAL SEQUENCE; CELL MEMBRANE; CELL STRAIN COS7; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYTOPLASM; DENTATORUBROPALLIDOLUYSIAN ATROPHY; ENZYME INHIBITION; GENE EXPRESSION REGULATION; HUMAN; HUMAN CELL; HUMAN CELL CULTURE; HUMAN TISSUE; IMMUNOCYTOCHEMISTRY; IMMUNOREACTIVITY; NEUROPATHOLOGY; PRIORITY JOURNAL; PROTEIN CLEAVAGE; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN PROCESSING;

ANIMALS; BASE SEQUENCE; BRAIN; CASPASES; CELL LINE; CERCOPITHECUS AETHIOPS; COS CELLS; DNA, COMPLEMENTARY; HUMANS; MODELS, BIOLOGICAL; MOLECULAR SEQUENCE DATA; MYOCLONIC EPILEPSIES, PROGRESSIVE; NERVE TISSUE PROTEINS; PEPTIDE FRAGMENTS; PEPTIDES; PROTEIN PROCESSING, POST-TRANSLATIONAL; RECOMBINANT PROTEINS; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 78449292904     PISSN: 1742464X     EISSN: 17424658     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2010.07893.x     Document Type: Article

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