Self-assembly of polyglutamine-containing huntingtin fragments into amyloid-like fibrils: Implications for Huntington's disease pathology

Proceedings of the National Academy of Sciences of the United States of America

Volumn 96, Issue 8, 1999, Pages 4604-4609

  Scherzinger, Eberhard ^b   Sittler, Annie ^b   Schweiger, Katja ^b   Heiser, Volker ^b   Lurz, Rudi ^b   Hasenbank, Renate ^b   Bates, Gillian P ^a   Lehrach, Hans ^b   Wanker, Erich E ^a,b  

^a MAX PLANCK INSTITUTE FOR MOLECULAR GENETICS   (Germany)

^b GUY S HOSPITAL   (United Kingdom)

Author keywords

Aggregation; Glutamine repeat; Huntingtin

Indexed keywords

HUNTINGTIN;

AMINO TERMINAL SEQUENCE; ARTICLE; EXON; HUNTINGTON CHOREA; MOLECULAR MODEL; PATHOGENESIS; PRION; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN ASSEMBLY; PROTEIN EXPRESSION; PROTEIN SYNTHESIS;

AMINO ACID SEQUENCE; AMYLOID; ANIMALS; CLONING, MOLECULAR; COS CELLS; ESCHERICHIA COLI; HUMANS; HUNTINGTON DISEASE; MOLECULAR SEQUENCE DATA; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDE FRAGMENTS; PEPTIDES; RECOMBINANT PROTEINS; TRANSFECTION;

SCRAPIE PRION;

EID: 0033551063     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.96.8.4604     Document Type: Article

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