Zinc-finger-based transcriptional repression of rhodopsin in a model of dominant retinitis pigmentosa

EMBO Molecular Medicine

Volumn 3, Issue 3, 2011, Pages 118-128

  Mussolino, Claudio ^a,d   Sanges, Daniela ^a   Marrocco, Elena ^a   Bonetti, Ciro ^a   Di Vicino, Umberto ^a   Marigo, Valeria ^b   Auricchio, Alberto ^a,c   Meroni, Germana ^a,e   Surace, Enrico Maria ^a  

^a TELETHON INSTITUTE OF GENETICS AND MEDICINE TIGEM   (Italy)

^b UNIVERSITY OF MODENA AND REGGIO EMILIA   (Italy)

^c UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^d HANNOVER MEDICAL SCHOOL   (Germany)

^e AREA Science Park   (Italy)

Author keywords

Gain of function; Retinitis pigmentosa; Transcriptional repression; Zinc finger

Indexed keywords

RHODOPSIN; ZINC FINGER PROTEIN;

ALLELE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL STRUCTURE; CONTROLLED STUDY; DISEASE COURSE; GENE REPRESSION; GENE SILENCING; GENETIC HETEROGENEITY; HUMAN; HUMAN CELL; HUMAN TISSUE; MOUSE; MUTANT; NONHUMAN; PHOTORECEPTOR; PRIORITY JOURNAL; RETINITIS PIGMENTOSA; TRANSCRIPTION REGULATION; TRANSGENIC MOUSE; WILD TYPE;

ANIMALS; DISEASE MODELS, ANIMAL; DOWN-REGULATION; GENE KNOCKDOWN TECHNIQUES; GENE THERAPY; HUMANS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; OPHTHALMOSCOPY; REPRESSOR PROTEINS; RETINITIS PIGMENTOSA; RHODOPSIN; TRANSCRIPTION, GENETIC;

EID: 79952097561     PISSN: 17574676     EISSN: 17574684     Source Type: Journal    
DOI: 10.1002/emmm.201000119     Document Type: Article

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