How i treat primary haemophagocytic lymphohistiocytosis

British Journal of Haematology

Volumn 182, Issue 2, 2018, Pages 185-199

  Marsh, Rebecca A ^a   Haddad, Elie ^b  

^a CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^b UNIVERSITY OF MONTREAL   (Canada)

Author keywords

haemophagocytic syndrome; immunodeficiency; immunology

Indexed keywords

ALEMTUZUMAB; CD27 ANTIGEN; CD4 ANTIGEN; CD8 ANTIGEN; CXCL9 CHEMOKINE; CYCLOSPORINE; DEXAMETHASONE; ETOPOSIDE; FERRITIN; FIBRINOGEN; GAMMA INTERFERON; HLA DR ANTIGEN; IMMUNOSUPPRESSIVE AGENT; INTERLEUKIN 18; METHOTREXATE; METHYLPREDNISOLONE; PERFORIN; RAS RELATED PROTEIN RAB 27A; RECOMBINANT INTERLEUKIN 18; RITUXIMAB; RUXOLITINIB; SIGNALING LYMPHOCYTE ACTIVATION MOLECULE ASSOCIATED PROTEIN; SOLUBLE INTERLEUKIN 2 RECEPTOR; STAT1 PROTEIN; THYMOCYTE ANTIBODY; TOCILIZUMAB; TRANSCRIPTION FACTOR GATA 2; TRIACYLGLYCEROL; UNINDEXED DRUG; X LINKED INHIBITOR OF APOPTOSIS;

ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION; APLASIA; BONE MARROW SUPPRESSION; CD27 GENE; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CLINICAL TRIAL (TOPIC); CYTOPENIA; FLOW CYTOMETRY; GENE; GENETIC DISORDER; HEMOPHAGOCYTIC SYNDROME; HEREDITY; HUMAN; HYPOPLASIA; LABORATORY TEST; MUTATIONAL ANALYSIS; NATURAL KILLER CELL; NEPHROTOXICITY; NONHUMAN; POSTERIOR REVERSIBLE ENCEPHALOPATHY SYNDROME; PRF1 GENE; PRIORITY JOURNAL; RAB27A GENE; REVIEW; SCREENING TEST; SH2D1A GENE; XIAP GENE; CHRONIC DISEASE; EARLY DIAGNOSIS; GENETICS; HEMATOPOIETIC STEM CELL TRANSPLANTATION; MULTIMODALITY CANCER THERAPY; MUTATION; PROCEDURES; TREATMENT OUTCOME;

CHRONIC DISEASE; COMBINED MODALITY THERAPY; EARLY DIAGNOSIS; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MUTATION; TREATMENT OUTCOME;

EID: 85049679524     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/bjh.15274     Document Type: Review

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