The Mitochondrial m-AAA Protease Prevents Demyelination and Hair Greying

PLoS Genetics

Volumn 12, Issue 12, 2016, Pages

  Wang, Shuaiyu ^a   Jacquemyn, Julie ^a   Murru, Sara ^a   Martinelli, Paola ^a   Barth, Esther ^a   Langer, Thomas ^a   Niessen, Carien M ^a   Rugarli, Elena I ^a  

^a UNIVERSITY OF COLOGNE   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

AFG3L2 PROTEIN; M AAA PROTEASE; MITOCHONDRIAL ENZYME; MYELIN; PROTEINASE; UNCLASSIFIED DRUG; ADENOSINE TRIPHOSPHATE DEPENDENT PROTEINASE; AFG3L1 PROTEIN, MOUSE; AFG3L2 PROTEIN, MOUSE; M-AAA PROTEASES; METALLOPROTEINASE;

AFG3L2 GENE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LOSS; CELL MATURATION; CELL SURVIVAL; CONTROLLED STUDY; DEMYELINATION; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME DEFICIENCY; FEMALE; GENE DELETION; HAIR DISCOLORATION; IN VIVO STUDY; MALE; MITOCHONDRION SWELLING; MOTOR DYSFUNCTION; MOUSE; NERVE CELL NECROSIS; NONHUMAN; OLIGODENDROGLIA; PARALOGY; PATHOPHYSIOLOGY; PROTEIN DEFECT; PROTEIN EXPRESSION; SCHWANN CELL; TARGET CELL; ANIMAL; BIOSYNTHESIS; CELL DEATH; DEMYELINATING DISEASE; GENETICS; GLIA; GROWTH, DEVELOPMENT AND AGING; HAIR; HUMAN; METABOLISM; MITOCHONDRION; MUTATION; MYELIN SHEATH; NERVE CELL; PATHOLOGY;

ANIMALS; ATP-DEPENDENT PROTEASES; CELL DEATH; CELL SURVIVAL; DEMYELINATING DISEASES; HAIR; HUMANS; METALLOENDOPEPTIDASES; MICE; MITOCHONDRIA; MUTATION; MYELIN SHEATH; NEUROGLIA; NEURONS; OLIGODENDROGLIA; SCHWANN CELLS;

EID: 85007553571     PISSN: 15537390     EISSN: 15537404     Source Type: Journal    
DOI: 10.1371/journal.pgen.1006463     Document Type: Article

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