Variable and tissue-specific subunit composition of mitochondrial m-AAA protease complexes linked to hereditary spastic paraplegia

Molecular and Cellular Biology

Volumn 27, Issue 2, 2007, Pages 758-767

  Koppen, Mirko ^a   Metodiev, Metodi D ^a   Casari, Giorgio ^b   Rugarli, Elena I ^c   Langer, Thomas ^a  

^a UNIVERSITY OF COLOGNE   (Germany)

^b SAN RAFFAELE HOSPITAL   (Italy)

^c DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

AAA PROTEINASE; ADENOSINE TRIPHOSPHATASE; MITOCHONDRIAL ENZYME; PARAPLEGIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BRAIN MITOCHONDRION; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME SPECIFICITY; ENZYME SUBUNIT; FIBROBLAST; HEREDITARY MOTOR SENSORY NEUROPATHY; MITOCHONDRIAL MEMBRANE; NERVE FIBER DEGENERATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN QUALITY; RIBOSOME;

ADENOSINE TRIPHOSPHATASES; ANIMALS; AXONS; BRAIN; HUMANS; HYDROLYSIS; METALLOENDOPEPTIDASES; MICE; MICE, KNOCKOUT; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; PROTEIN SUBUNITS; SACCHAROMYCES CEREVISIAE; SACCHAROMYCES CEREVISIAE PROTEINS; SPASTIC PARAPLEGIA, HEREDITARY;

EID: 33846127778     PISSN: 02707306     EISSN: None     Source Type: Journal    
DOI: 10.1128/MCB.01470-06     Document Type: Article

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