Molecular neuropathology of the synapse in sheep with CLN5 Batten disease

Brain and Behavior

Volumn 5, Issue 11, 2015, Pages

  Amorim, Inês S ^a   Mitchell, Nadia L ^b   Palmer, David N ^b   Sawiak, Stephen J ^c,d   Mason, Roger ^c   Wishart, Thomas M ^a,e   Gillingwater, Thomas H ^a  

^a UNIVERSITY OF EDINBURGH   (United Kingdom)

^b LINCOLN UNIVERSITY   (New Zealand)

^c UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^d ADDENBROOKE S HOSPITAL   (United Kingdom)

^e UNIVERSITY OF EDINBURGH   (United Kingdom)

Author keywords

Animal model; Lysosomal storage disorders; Neurodegeneration; Neuronal ceroid lipofuscinoses; Neuronal ceroid lipofuscinosis; Sheep; Synapse; Synaptic vulnerability

Indexed keywords

2',3' CYCLIC NUCLEOTIDE 3' PHOSPHODIESTERASE; ALPHA SYNUCLEIN; CALRETININ; CYSTEINE; CYSTEINE STRING PROTEIN ALPHA; NEUROFASCIN; PROTEIN; ROCK2 PROTEIN; SIRTUIN 2; UBIQUITIN PROTEIN LIGASE E3; UBR4 PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ATROPHY; AUTOPSY; BRAIN SYNAPTOSOME; CEREBELLUM; CLINICAL TRIAL (TOPIC); CONTROLLED STUDY; CORTICAL THICKNESS (BRAIN); DEGENERATIVE DISEASE; DROSOPHILA; GEL ELECTROPHORESIS; MOTOR CORTEX; MOUSE; NEURONAL CEROID LIPOFUSCINOSIS; NEUROPATHOLOGY; NONHUMAN; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN EXPRESSION; SHEEP; SYNAPSE; SYNAPTIC EFFICACY; WESTERN BLOTTING; ANIMAL; BRAIN CORTEX; DISEASE MODEL; FEMALE; MALE; PATHOLOGY; SHEEP DISEASE;

ANIMALS; CEREBELLUM; CEREBRAL CORTEX; DISEASE MODELS, ANIMAL; FEMALE; MALE; NEURONAL CEROID-LIPOFUSCINOSES; SHEEP; SHEEP DISEASES; SYNAPSES;

EID: 84954377568     PISSN: None     EISSN: 21623279     Source Type: Journal    
DOI: 10.1002/brb3.401     Document Type: Article

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