Batten disease (JNCL) is linked to disturbances in mitochondrial, cytoskeletal, and synaptic compartments

Journal of Neuroscience Research

Volumn 84, Issue 5, 2006, Pages 1124-1138

  Luiro, Kaisu ^a   Kopra, Outi ^a,b   Blom, Tomas ^c   Gentile, Massimiliano ^b   Mitchison, Hannah M ^d   Hovatta, Iiris ^a   Törnquist, Kid ^c,e   Jalanko, Anu ^a  

^a NATIONAL PUBLIC HEALTH INSTITUTE   (Finland)

^b UNIVERSITY OF HELSINKI   (Finland)

^c ÅBO AKADEMI UNIVERSITY   (Finland)

^d ROYAL FREE AND UNIVERSITY COLLEGE MEDICAL SCHOOL   (United Kingdom)

^e MINERVA FOUNDATION INSTITUTE FOR MEDICAL RESEARCH   (Finland)

Author keywords

CLN3; Cytosketeton; Lysosomal; Neurodegenerative disease, mitochondria; Synaptosome

Indexed keywords

CALCIUM CHANNEL; GUANINE NUCLEOTIDE BINDING PROTEIN BETA SUBUNIT; VOLTAGE GATED CALCIUM CHANNEL;

ARTICLE; BRAIN SYNAPTOSOME; CELL MEMBRANE DEPOLARIZATION; CLN3 GENE; CONTROLLED STUDY; CYTOSKELETON; DNA MICROARRAY; GENE; GENE EXPRESSION; GLUCOSE METABOLISM; MITOCHONDRION; MOUSE; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; REAL TIME POLYMERASE CHAIN REACTION; SYNAPTIC TRANSMISSION; UNINDEXED SEQUENCE;

ANIMALS; CALCIUM; CELLS, CULTURED; CYTOSKELETON; DISEASE MODELS, ANIMAL; DOWN-REGULATION; EMBRYO; EMBRYO, MAMMALIAN; GENE EXPRESSION; GENE EXPRESSION PROFILING; IMMUNOHISTOCHEMISTRY; MEMBRANE GLYCOPROTEINS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROSCOPY, ELECTRON, TRANSMISSION; MICROTUBULE-ASSOCIATED PROTEINS; MITOCHONDRIA; MOLECULAR CHAPERONES; MUTATION; NEURONAL CEROID-LIPOFUSCINOSES; NEURONS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; SYNAPSES;

EID: 33749495207     PISSN: 03604012     EISSN: 10974547     Source Type: Journal    
DOI: 10.1002/jnr.21015     Document Type: Article

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