The neuronal ceroid lipofuscinoses: The same, but different?

Biochemical Society Transactions

Volumn 38, Issue 6, 2010, Pages 1448-1452

  Cooper, Jonathan D ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

Batten disease; Lysosomal dysfunction; Lysosomal storage disorder (LSD) neuroimmune response; Neuronal ceroid lipofuscinosis (NCL); Selective neuron vulnerability

Indexed keywords

SNARE PROTEIN;

ASTROCYTE; ASTROCYTOSIS; BRAIN NERVE CELL; CELL ACTIVATION; CELL LOSS; CONFERENCE PAPER; GLIA; HUMAN; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PATHOGENESIS; PRESYNAPTIC MEMBRANE; PRIORITY JOURNAL; THALAMOCORTICAL TRACT;

ANIMALS; BRAIN; DISEASE MODELS, ANIMAL; HUMANS; MICE; NERVE DEGENERATION; NEURONAL CEROID-LIPOFUSCINOSES; NEURONS;

ANIMALIA;

EID: 78649747041     PISSN: 03005127     EISSN: 14708752     Source Type: Journal    
DOI: 10.1042/BST0381448     Document Type: Conference Paper

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