Small peptides against the mutant SOD1/Bcl-2 toxic mitochondrial complex restore mitochondrial function and cell viability in mutant SOD1-mediated ALS

Journal of Neuroscience

Volumn 33, Issue 28, 2013, Pages 11588-11598

  Tan, Wenzhi ^a   Naniche, Nicole ^a   Bogush, Alexey ^a   Pedrini, Steve ^a   Trotti, Davide ^a   Pasinelli, Piera ^a  

^a THOMAS JEFFERSON UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; PROTEIN BCL 2; VOLTAGE DEPENDENT ANION CHANNEL 1;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ARTICLE; CELL LOSS; CELL VIABILITY; CONFOCAL MICROSCOPY; DELETION MUTANT; DISEASE COURSE; FEMALE; FLOW CYTOMETRY; HUMAN; HUMAN CELL; HYPERPOLARIZATION; IMMUNOFLUORESCENCE TEST; MALE; MEMBRANE PERMEABILITY; MITOCHONDRION; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN INTERACTION; TRANSGENIC MOUSE; TRANSMISSION ELECTRON MICROSCOPY; WESTERN BLOTTING;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL SURVIVAL; FEMALE; HEK293 CELLS; HUMANS; MALE; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MITOCHONDRIA; MUTATION; PEPTIDE FRAGMENTS; PROTEIN BINDING; PROTO-ONCOGENE PROTEINS C-BCL-2; SUPEROXIDE DISMUTASE;

EID: 84880430220     PISSN: 02706474     EISSN: 15292401     Source Type: Journal    
DOI: 10.1523/JNEUROSCI.5385-12.2013     Document Type: Article

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