Secondary biochemical and morphological consequences in lysosomal storage diseases

Biochemistry (Moscow)

Volumn 79, Issue 7, 2014, Pages 619-636

  Alroy, J ^a   Garganta, C ^b   Wiederschain, G ^c  

^a TUFTS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b TUFTS MEDICAL CENTER   (United States)

^c BOSTON COLLEGE   (United States)

Author keywords

autophagy; deficiency of lysosomal enzymes and protein cofactors; lysosomal storage diseases; lysosomes; metabolic correction; pathogenic cascades; recycling

Indexed keywords

CALCIUM; GLYCOPROTEIN; GLYCOSAMINOGLYCAN;

ANIMAL; AUTOPHAGY; ENZYMOLOGY; EXTRACELLULAR MATRIX; HUMAN; LYSOSOME; LYSOSOME STORAGE DISEASE; METABOLISM; PATHOLOGY; PHYSIOLOGY;

ANIMALS; AUTOPHAGY; CALCIUM; EXTRACELLULAR MATRIX; GLYCOPROTEINS; GLYCOSAMINOGLYCANS; HUMANS; LYSOSOMAL STORAGE DISEASES; LYSOSOMES;

EID: 84906256999     PISSN: 00062979     EISSN: 16083040     Source Type: Journal    
DOI: 10.1134/S0006297914070049     Document Type: Review

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