Peripheral neuropathy in the twitcher mouse: Accumulation of extracellular matrix in the endoneurium and aberrant expression of ion channels

Acta Neuropathologica

Volumn 115, Issue 5, 2008, Pages 577-587

  Kagitani Shimono, Kuriko ^a,b   Mohri, Ikuko ^a,b   Yagi, Takashi ^a   Taniike, Masako ^b   Suzuki, Kinuko ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b OSAKA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Bone marrow transplantation; Demyelination; Krabbe's disease; Node of Ranvier; Remyelination

Indexed keywords

ALCIAN BLUE; GLIAL FIBRILLARY ACIDIC PROTEIN; ION CHANNEL; MEMBRANE PROTEIN; NEUREXIN IV CASPR PARANOIDIN 1; POTASSIUM CHANNEL; SODIUM CHANNEL; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE MARROW TRANSPLANTATION; CONTROLLED STUDY; ENDONEURIUM; EXTRACELLULAR MATRIX; GLOBOID CELL LEUKODYSTROPHY; MOUSE; NERVE FIBER; NONHUMAN; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; PROTEIN EXPRESSION; RANVIER NODE; SCHWANN CELL; SCIATIC NERVE; THERAPY EFFECT; WILD TYPE;

ANIMALS; BONE MARROW TRANSPLANTATION; DISEASE MODELS, ANIMAL; EXTRACELLULAR MATRIX; FIBRONECTINS; INDOLES; LAMININ; LEUKODYSTROPHY, GLOBOID CELL; MICE; MICE, NEUROLOGIC MUTANTS; MICROSCOPY, ELECTRON, TRANSMISSION; MYELIN SHEATH; NERVE TISSUE PROTEINS; PERIPHERAL NERVES; PERIPHERAL NERVOUS SYSTEM DISEASES; RANVIER'S NODES;

EID: 41949112547     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-007-0333-3     Document Type: Article

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