Immune system irregularities in lysosomal storage disorders

Acta Neuropathologica

Volumn 115, Issue 2, 2008, Pages 159-174

  Castaneda, Julian A ^a   Lim, Ming J ^b   Cooper, Jonathan D ^b   Pearce, David A ^a  

^a UNIVERSITY OF ROCHESTER SCHOOL OF MEDICINE AND DENTISTRY   (United States)

^b KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA MANNOSIDASE; BETA GLUCURONIDASE; BETA N ACETYLHEXOSAMINIDASE A; BETA N ACETYLHEXOSAMINIDASE B; CD3 ANTIGEN; CD4 ANTIGEN; CD8 ANTIGEN; GALACTOSYLCERAMIDASE; GANGLIOSIDE GM2; GLUCOSYLCERAMIDASE; GLUTAMATE DECARBOXYLASE 65; GLUTAMATE DECARBOXYLASE 65 ANTIBODY; GLYCOSAMINOGLYCAN; INTERLEUKIN 10; INTERLEUKIN 2 RECEPTOR; MACROPHAGE INFLAMMATORY PROTEIN 1ALPHA; MACROPHAGE INFLAMMATORY PROTEIN 1BETA; MAJOR HISTOCOMPATIBILITY ANTIGEN CLASS 1; MAJOR HISTOCOMPATIBILITY ANTIGEN CLASS 2; MEMBRANE PROTEIN; MONOCYTE CHEMOTACTIC PROTEIN 1; N ACETYLGLUCOSAMINYLTRANSFERASE; PROTEOLIPID; PSYCHOSINE; PYRUVATE DEHYDROGENASE; SPHINGOMYELIN PHOSPHODIESTERASE; TUMOR NECROSIS FACTOR ALPHA; TUMOR NECROSIS FACTOR ALPHA RECEPTOR;

BLOOD BRAIN BARRIER; BONE DISEASE; CYTOTOXIC T LYMPHOCYTE; DISEASE SEVERITY; ENZYME ACTIVITY; ENZYME DEFICIENCY; GAUCHER DISEASE; GENE DELETION; GENE MUTATION; GLOBOID CELL LEUKODYSTROPHY; GM2 GANGLIOSIDOSIS; HEPATOSPLENOMEGALY; HUMAN; IMMUNE DEFICIENCY; IMMUNE RESPONSE; IMMUNE SYSTEM; LYSOSOME STORAGE DISEASE; MANNOSIDOSIS; MUCOPOLYSACCHARIDOSIS TYPE 7; NATURAL KILLER T CELL; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NIEMANN PICK DISEASE; NONHUMAN; PATHOGENESIS; PERIPHERAL BLOOD MONONUCLEAR CELL; PRIORITY JOURNAL; REVIEW; SANDHOFF DISEASE; TAY SACHS DISEASE;

ANIMALS; HUMANS; LYSOSOMAL STORAGE DISEASES;

EID: 38149018555     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-007-0296-4     Document Type: Review

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