Mitochondrial dysfunction in the neuronal ceroid-lipofuscinoses (Batten disease)

Neurochemistry International

Volumn 40, Issue 6, 2002, Pages 565-571

  Jolly, R D ^a   Brown, S ^a   Das, A M ^b   Walkley, S U ^c  

^a MASSEY UNIVERSITY   (New Zealand)

^b Zentrum Kinderheilkunde und Humangenetik   (Germany)

^c ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

ATP synthase; Batten disease; Ceroid lipofuscinosis; Excitotoxicity; Mitochondria; Subunit c

Indexed keywords

PHOSPHATE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

ARTICLE; CLINICAL FEATURE; DEGENERATIVE DISEASE; DISEASE ASSOCIATION; DISEASE MODEL; DISEASE SEVERITY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DOG; ENZYME SUBUNIT; FIBROBLAST; FUNCTION TEST; GENETIC DISORDER; HUMAN; HYPOTHESIS; LIVER MITOCHONDRION; LYSOSOME STORAGE DISEASE; MITOCHONDRIAL ENERGY TRANSFER; MITOCHONDRIAL RESPIRATION; NERVE CELL; NERVE CELL NECROSIS; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NEUROTOXICITY; NOMENCLATURE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; SHEEP; STRUCTURE ANALYSIS;

ANIMALS; DOGS; ENERGY METABOLISM; HUMANS; MITOCHONDRIA; NERVE DEGENERATION; NEURONAL CEROID-LIPOFUSCINOSES; SHEEP;

ANIMALIA; CANIS FAMILIARIS; OVIS ARIES;

EID: 0036176571     PISSN: 01970186     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0197-0186(01)00128-0     Document Type: Article

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