Secondary alterations of sphingolipid metabolism in lysosomal storage diseases

Neurochemical Research

Volumn 36, Issue 9, 2011, Pages 1654-1668

  Prinetti, Alessandro ^a   Prioni, Simona ^a   Chiricozzi, Elena ^a   Schuchman, Edward H ^b   Chigorno, Vanna ^a   Sonnino, Sandro ^a  

^a UNIVERSITY OF MILAN   (Italy)

^b MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

Gangliosides; Glycosphingolipids; Niemann Pick disease; Sphingolipidosis; Sphingolipids; Sphingomyelin

Indexed keywords

GANGLIOSIDE GM1; GANGLIOSIDE GM2; GANGLIOSIDE GM3; MIGLUSTAT; PHOSPHATIDYLCHOLINE; PHOSPHATIDYLETHANOLAMINE; PHOSPHATIDYLINOSITOL; PHOSPHATIDYLSERINE; SPHINGOLIPID; SPHINGOMYELIN; SPHINGOMYELIN PHOSPHODIESTERASE;

ARTICLE; BRAIN; BRAIN STEM; CEREBELLUM; ENDOPLASMIC RETICULUM STRESS; GAUCHER DISEASE; HIGH PERFORMANCE THIN LAYER CHROMATOGRAPHY; HUMAN; KIDNEY; LIPID COMPOSITION; LIPID METABOLISM; LIPIDOSIS; LIVER; LYSOSOME STORAGE DISEASE; NIEMANN PICK DISEASE; NONHUMAN; PANCREAS; PRIORITY JOURNAL; SPHINGOLIPID METABOLISM; SPLEEN; TAY SACHS DISEASE; TISSUE SPECIFICITY;

ANIMALS; GANGLIOSIDES; GLYCOSYLTRANSFERASES; LIPID METABOLISM; LYSOSOMAL STORAGE DISEASES; NERVOUS SYSTEM; NEURODEGENERATIVE DISEASES; NIEMANN-PICK DISEASES; SPHINGOLIPIDS; TISSUE DISTRIBUTION;

ANIMALIA;

EID: 80755129000     PISSN: 03643190     EISSN: 15736903     Source Type: Journal    
DOI: 10.1007/s11064-010-0380-3     Document Type: Article

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