NRIP1/RIP140 siRNA-mediated attenuation counteracts mitochondrial dysfunction in down syndrome

Human Molecular Genetics

Volumn 23, Issue 16, 2014, Pages 4406-4419

  Izzo, Antonella ^a   Manco, Rosanna ^a   Bonfiglio, Ferdinando ^a   Calì, Gaetano ^b   de Cristofaro, Tiziana ^b   Patergnani, Simone ^c   Cicatiello, Rita ^a   Scrima, Rosella ^d   Zannini, Mariastella ^b   Pinton, Paolo ^c   Conti, Anna ^a   Nitsch, Lucio ^a  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^b CNR   (Italy)

^c UNIVERSITY OF FERRARA   (Italy)

^d UNIVERSITY OF FOGGIA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; CALCIUM ION; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; REACTIVE OXYGEN METABOLITE; RECEPTOR INTERACTING PROTEIN 140; SMALL INTERFERING RNA; CALCIUM; NUCLEAR PROTEIN; PPARGC1A PROTEIN, HUMAN; SIGNAL TRANSDUCING ADAPTOR PROTEIN; TRANSCRIPTION FACTOR;

AEROBIC METABOLISM; ARTICLE; BIOGENESIS; CALCIUM HOMEOSTASIS; DISEASES; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DOWN SYNDROME; FETUS HEART; FIBROBLAST; GENE ONTOLOGY; GENE OVEREXPRESSION; MITOCHONDRIAL GENE; NUCLEAR ENCODED MITOCHONDRIAL GENE; PRIORITY JOURNAL; RECEPTOR DOWN REGULATION; CARDIAC MUSCLE; CELL CULTURE; CHROMOSOME 21; CYTOLOGY; FETUS DEATH; HUMAN; META ANALYSIS; METABOLISM; MITOCHONDRION; PHYSIOLOGY; TRISOMY;

ABORTED FETUS; ADAPTOR PROTEINS, SIGNAL TRANSDUCING; ADENOSINE TRIPHOSPHATE; CALCIUM; CELLS, CULTURED; CHROMOSOMES, HUMAN, PAIR 21; DOWN SYNDROME; FIBROBLASTS; GENES, MITOCHONDRIAL; HUMANS; MITOCHONDRIA; MYOCARDIUM; NUCLEAR PROTEINS; RNA, SMALL INTERFERING; TRANSCRIPTION FACTORS; TRISOMY;

EID: 84904766755     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddu157     Document Type: Article

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