Chaperones and cardiac misfolding protein diseases

Current Protein and Peptide Science

Volumn 15, Issue 3, 2014, Pages 189-204

  Christians, Elisabeth S ^a   Mustafi, Soumyajit B ^a   Benjamin, Ivor J ^a  

^a UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

Author keywords

Aggregates; Amyloid; Cardiomyocyte; Heat shock factor; Heat shock proteins; Homeostasis; Mouse models; Mutation

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 6; ALPHA CRYSTALLIN; BETA CATENIN; CHAPERONE; CHAPERONIN 60; CHAPERONIN CONTAINING TCP1; CONNEXIN 43; DESMOPLAKIN; EARLY PREGNANCY FACTOR; HEAT SHOCK COGNATE PROTEIN 70; HEAT SHOCK PROTEIN 110; HEAT SHOCK PROTEIN 20; HEAT SHOCK PROTEIN 22; HEAT SHOCK PROTEIN 27; HEAT SHOCK PROTEIN 40; HEAT SHOCK PROTEIN 70; HEAT SHOCK PROTEIN 90; HEAT SHOCK TRANSCRIPTION FACTOR 1; POTASSIUM CHANNEL HERG; PROTEIN P53; PROTEIN P62; SMALL HEAT SHOCK PROTEIN; TROPONIN I; TUMOR NECROSIS FACTOR ALPHA; UBIQUITIN PROTEIN LIGASE E3; HEAT SHOCK PROTEIN;

AUTOPHAGY; CARDIAC PROTEIN MISFOLDING; CELL DEATH; CELLULAR STRESS RESPONSE; CONGESTIVE CARDIOMYOPATHY; CYSTIC FIBROSIS; ENDOPLASMIC RETICULUM STRESS; GASTRULATION; GENE MUTATION; HEART MUSCLE CELL; HEART VENTRICLE HYPERTROPHY; HUNTINGTON CHOREA; LONG QT SYNDROME 2; LOSS OF FUNCTION MUTATION; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN HOMEOSTASIS; PROTEIN LOCALIZATION; REVIEW; UNFOLDED PROTEIN RESPONSE; ANIMAL; CHEMISTRY; GENETICS; HEART DISEASE; HUMAN; METABOLISM; PROTEOSTASIS DEFICIENCY;

ANIMALS; HEART DISEASES; HEAT-SHOCK PROTEINS; HUMANS; MOLECULAR CHAPERONES; PROTEOSTASIS DEFICIENCIES;

EID: 84904469376     PISSN: 13892037     EISSN: 18755550     Source Type: Journal    
DOI: 10.2174/1389203715666140331111518     Document Type: Review

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