Active HSF1 significantly suppresses polyglutamine aggregate formation in cellular and mouse models

Journal of Biological Chemistry

Volumn 280, Issue 41, 2005, Pages 34908-34916

  Fujimoto, Mitsuaki ^a   Takaki, Eiichi ^a   Hayashi, Tetsuya ^b   Kitaura, Yasushi ^b   Tanaka, Yasunori ^a   Inouye, Sachiye ^a   Nakai, Akira ^a  

^a YAMAGUCHI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b OSAKA MEDICAL COLLEGE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

BRAIN; CELLS; DISEASE CONTROL; ENZYME INHIBITION; MUSCLE; NEUROLOGY;

CELL DEATH; CULTURE CELLS; INCLUSION FORMATION; NEURODEGENERATIVE DISEASES;

AMINES;

HEAT SHOCK PROTEIN; HEAT SHOCK TRANSCRIPTION FACTOR 1; POLYGLUTAMINE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL DEATH; CELL INCLUSION; CONTROLLED STUDY; DEGENERATIVE DISEASE; DISEASE MODEL; FEMALE; GENE EXPRESSION REGULATION; GENE OVEREXPRESSION; HEAT SHOCK; HUMAN; HUMAN CELL; HUNTINGTON CHOREA; IN VITRO STUDY; IN VIVO STUDY; LIFESPAN; MALE; MOUSE; NONHUMAN; NUCLEOTIDE REPEAT; POLYAMINE METABOLISM; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN FOLDING; PROTEIN INDUCTION; PROTEIN PROTEIN INTERACTION; SKELETAL MUSCLE; TRANSGENIC MOUSE; WEIGHT REDUCTION;

MUS MUSCULUS;

EID: 27144524290     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M506288200     Document Type: Article

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